Literature DB >> 28410093

Race, Income, and Disease Outcomes in Juvenile Dermatomyositis.

Kathryn Phillippi1, Mark Hoeltzel2, Angela Byun Robinson3, Susan Kim4.   

Abstract

OBJECTIVE: To determine the relationships among race, income, and disease outcomes in children with juvenile dermatomyositis (JDM). STUDY
DESIGN: Data from 438 subjects with JDM enrolled in the Childhood Arthritis and Rheumatology Research Alliance (CARRA) Legacy Registry were analyzed. Demographic data included age, sex, race, annual family income, and insurance status. Clinical outcomes included muscle strength, presence of rash, calcinosis, weakness, physical function, and quality of life measures. Disease outcomes were compared based on race and income.
RESULTS: Minority subjects were significantly more likely to have low annual family income and significantly worse scores on measures of physical function, disease activity, and quality of life measures. Subjects with lower annual family income had worse scores on measures of physical function, disease activity, and quality of life scores, as well as weakness. Black subjects were more likely to have calcinosis. Despite these differences in outcome measures, there were no significant differences among the racial groups in time to diagnosis or duration of disease. Using calcinosis as a marker of disease morbidity, black race, annual family income <$50 000 per year, negative antinuclear antibody, and delay in diagnosis >12 months were associated with calcinosis.
CONCLUSION: Minority race and lower family income are associated with worse morbidity and outcomes in subjects with JDM. Calcinosis was more common in black subjects. Further studies are needed to examine these associations in more detail, to support efforts to address health disparities in subjects with JDM and improve disease outcomes.
Copyright © 2017 Elsevier Inc. All rights reserved.

Entities:  

Keywords:  JDM; calcinosis; health disparities; juvenile dermatomyositis

Mesh:

Year:  2017        PMID: 28410093      PMCID: PMC5410644          DOI: 10.1016/j.jpeds.2017.01.046

Source DB:  PubMed          Journal:  J Pediatr        ISSN: 0022-3476            Impact factor:   4.406


  36 in total

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7.  Clinical characteristics of children with juvenile dermatomyositis: the Childhood Arthritis and Rheumatology Research Alliance Registry.

Authors:  Angela Byun Robinson; Mark F Hoeltzel; Dawn M Wahezi; Mara L Becker; Elizabeth A Kessler; Heinrike Schmeling; Ruy Carrasco; Adam M Huber; Brian M Feldman; Ann M Reed
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Review 8.  Calcinosis Biomarkers in Adult and Juvenile Dermatomyositis.

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