Literature DB >> 1163071

Fanconi's anemia. I. Case histories, clinical and laboratory findings in six affected siblings.

G Prindull, P Stubbe, W Kratzer.   

Abstract

This is a study of the largest family with Fanconi's anemia known in the world literature, namely of 6 affected siblings. All patients showed the typical features of the disease, including pancytopenia, skeletal and kidney deformities, hyperpigmentation of the skin, and physical as well as mental retardation. Four of the patients have died of their disease, the 2 patients who are still living at present have a deteriorating clinical course. Case histories, clinical and laboratory findings are reported here. In the second and third part of this study [48, 52] endocrinologic and genetic findings will be reported.

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Year:  1975        PMID: 1163071

Source DB:  PubMed          Journal:  Z Kinderheilkd        ISSN: 0044-2917


  7 in total

1.  No abnormalities in the NAD+ ADP-ribosyltransferase (polymerizing) gene of transformed cells from a Fanconi's anemia patient.

Authors:  K Flick; R Schneider; B Auer; M Hirsch-Kauffmann; M Schweiger
Journal:  Hum Genet       Date:  1992-08       Impact factor: 4.132

2.  Formal genetics of Fanconi's anemia.

Authors:  T M Schroeder; D Tilgen; J Krüger; F Vogel
Journal:  Hum Genet       Date:  1976-06-29       Impact factor: 4.132

3.  Endocrine studies in Fanconi's anaemia. Report of 4 cases.

Authors:  A Aynsley-Green; M Zachmann; E A Werder; R Illig; A Prader
Journal:  Arch Dis Child       Date:  1978-02       Impact factor: 3.791

4.  Antagonistic effect of cocultivation on mitomycin C-induced aberration rate in cells of a patient with Fanconi's anemia and in Chinese hamster ovary cells.

Authors:  S Zakrzewski; K Sperling
Journal:  Hum Genet       Date:  1980       Impact factor: 4.132

5.  Deficiency of DNA ligase activity in Fanconi's anemia.

Authors:  M Hirsch-Kauffmann; M Schweiger; E F Wagner; K Sperling
Journal:  Hum Genet       Date:  1978-11-24       Impact factor: 4.132

6.  Spectrum of anomalies in Fanconi anaemia.

Authors:  A Glanz; F C Fraser
Journal:  J Med Genet       Date:  1982-12       Impact factor: 6.318

7.  DNA repair dependent NAD+ metabolism is impaired in cells from patients with Fanconi's anemia.

Authors:  H Klocker; B Auer; M Hirsch-Kauffmann; H Altmann; H J Burtscher; M Schweiger
Journal:  EMBO J       Date:  1983       Impact factor: 11.598

  7 in total

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