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Literature DB >> 8828628

Recommendations for protein and amino acid intake in phenylketonuria patients.

Abstract

Nitrogen requirement in phenylketonuria patients is similar to that of normal persons. Prescribed protein intake for patients should be based on age-related safe levels of protein intake modified by the digestibility-corrected amino acid score. Adequate energy intakes and distribution of dietary protein over meals are important determinants for the quality of dietary treatment.

Entities: Chemical Disease Species

Mesh：

Substances：

Year: 1996 PMID： 8828628 DOI： 10.1007/pl00014229

Source DB: PubMed Journal: Eur J Pediatr ISSN： 0340-6199 Impact factor: 3.183

5 in total

1. Effect on nitrogen balance of adult man of varying source of nitrogen and level of calorie intake.

Authors: H L Anderson; M B Heindel; H Linkswiler
Journal: J Nutr Date: 1969-09 Impact factor: 4.798

2. Energy and protein requirements. Report of a joint FAO/WHO/UNU Expert Consultation.

Authors:
Journal: World Health Organ Tech Rep Ser Date: 1985

3. Acute illness in maple syrup urine disease: dynamics of protein metabolism and implications for management.

Authors: G N Thompson; D E Francis; D Halliday
Journal: J Pediatr Date: 1991-07 Impact factor: 4.406

4. Decreased essential amino acid requirements without catabolism in phenylketonuria and maple syrup urine disease.

Authors: T Ruch; D Kerr
Journal: Am J Clin Nutr Date: 1982-02 Impact factor: 7.045

5. Plasma amino acid response to ingestion of L-amino acids and whole protein.

Authors: S S Gropper; D M Gropper; P B Acosta
Journal: J Pediatr Gastroenterol Nutr Date: 1993-02 Impact factor: 2.839

5 in total

1. The intake of total protein, natural protein and protein substitute and growth of height and head circumference in Dutch infants with phenylketonuria.

Authors: M Hoeksma; M Van Rijn; P H Verkerk; A M Bosch; M F Mulder; J B C de Klerk; T J de Koning; E Rubio-Gozalbo; M de Vries; P J J Sauer; F J van Spronsen
Journal: J Inherit Metab Dis Date: 2005 Impact factor: 4.982

Recommendations for protein and amino acid intake in phenylketonuria patients.

1. Effect on nitrogen balance of adult man of varying source of nitrogen and level of calorie intake.

2. Energy and protein requirements. Report of a joint FAO/WHO/UNU Expert Consultation.

3. Acute illness in maple syrup urine disease: dynamics of protein metabolism and implications for management.

4. Decreased essential amino acid requirements without catabolism in phenylketonuria and maple syrup urine disease.

5. Plasma amino acid response to ingestion of L-amino acids and whole protein.

1. The intake of total protein, natural protein and protein substitute and growth of height and head circumference in Dutch infants with phenylketonuria.

Review 2. Protein substitutes for PKU: what's new?

Review 3. The truth of treating patients with phenylketonuria after childhood: the need for a new guideline.

4. Protein substitute dosage in PKU: how much do young patients need?

Review 5. Protein Substitutes in PKU; Their Historical Evolution.