Literature DB >> 34038570

Polygenic Risk Score for Alzheimer's Disease in Caribbean Hispanics.

Richard Mayeux1,2,3,4,5, Giuseppe Tosto1,2,3, Sanjeev Sariya1,2,3, Daniel Felsky6, Dolly Reyes-Dumeyer1,2,3, Ricky Lali7, Rafael A Lantigua1,4, Badri Vardarajan1,2,3, Ivonne Z Jiménez-Velázquez8, Jonathan L Haines9, Gerard D Shellenberg10, Margaret A Pericak-Vance11, Guillaume Paré7.   

Abstract

OBJECTIVE: Polygenic risk scores (PRSs) assess the individual genetic propensity to a condition by combining sparse information scattered across genetic loci, often displaying small effect sizes. Most PRSs are constructed in European-ancestry populations, limiting their use in other ethnicities. Here we constructed and validated a PRS for late-onset Alzheimer's Disease (LOAD) in Caribbean Hispanics (CH).
METHODS: We used a CH discovery (n = 4,312) and independent validation sample (n = 1,850) to construct an ancestry-specific PRS ("CH-PRS") and evaluated its performance alone and with other predictors using the area under curve (AUC) and logistic regression (strength of association with LOAD and statistical significance). We tested if CH-PRS predicted conversion to LOAD in a subsample with longitudinal data (n = 1,239). We also tested the CH-PRS in an independent replication CH cohort (n = 200) and brain autopsy cohort (n = 33). Finally, we tested the effect of ancestry on PRS by using European and African American discovery cohorts to construct alternative PRSs ("EUR-PRS", "AA-PRS").
RESULTS: The full model (LOAD ~ CH-PRS + sex + age + APOE-ɛ4), achieved an AUC = 74% (ORCH-PRS  = 1.51 95%CI = 1.36-1.68), raising to >75% in APOE-ɛ4 non-carriers. CH-PRS alone achieved an AUC = 72% in the autopsy cohort, raising to AUC = 83% in full model. Higher CH-PRS was significantly associated with clinical LOAD in the replication CH cohort (OR = 1.61, 95%CI = 1.19-2.17) and significantly predicted conversion to LOAD (HR = 1.93, CI = 1.70-2.20) in the longitudinal subsample. EUR-PRS and AA-PRS reached lower prediction accuracy (AUC = 58% and 53%, respectively).
INTERPRETATION: Enriching diversity in genetic studies is critical to provide an effective PRS in profiling LOAD risk across populations. ANN NEUROL 2021;90:366-376.
© 2021 American Neurological Association.

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Year:  2021        PMID: 34038570      PMCID: PMC8435026          DOI: 10.1002/ana.26131

Source DB:  PubMed          Journal:  Ann Neurol        ISSN: 0364-5134            Impact factor:   11.274


  40 in total

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