[A rare manifestation of an inflammatory rheumatic systemic disease].

Granulomatosis with polyangiitis (GPA) is an ANCA(anti-neutrophil cytoplasmatic antibody)-associated small vessel vasculitis usually affecting the respiratory tract and the kidneys. This article reports on a 46-year-old male patient with a rare organ manifestation pattern of GPA: besides a fulminantly progressive tetraparesis the patient suffered from severe ulcerative colitis. The early diagnosis of GPA with unusual findings and its delineation from a septic event is essential.