Literature DB >> 27037229

ABCA7 rare variants and Alzheimer disease risk.

Kilan Le Guennec1, Gaël Nicolas1, Olivier Quenez1, Camille Charbonnier1, David Wallon1, Céline Bellenguez1, Benjamin Grenier-Boley1, Stéphane Rousseau1, Anne-Claire Richard1, Anne Rovelet-Lecrux1, Delphine Bacq1, Jean-Guillaume Garnier1, Robert Olaso1, Anne Boland1, Vincent Meyer1, Jean-François Deleuze1, Philippe Amouyel1, Hans Markus Munter1, Guillaume Bourque1, Mark Lathrop1, Thierry Frebourg1, Richard Redon1, Luc Letenneur1, Jean-François Dartigues1, Florence Pasquier1, Adeline Rollin-Sillaire1, Emmanuelle Génin1, Jean-Charles Lambert1, Didier Hannequin1, Dominique Campion.   

Abstract

OBJECTIVE: To study the association between ABCA7 rare coding variants and Alzheimer disease (AD) in a case-control setting.
METHODS: We conducted a whole exome analysis among 484 French patients with early-onset AD and 590 ethnically matched controls.
RESULTS: After collapsing rare variants (minor allele frequency ≤1%), we detected an enrichment of ABCA7 loss of function (LOF) and predicted damaging missense variants in cases (odds ratio [OR] 3.40, 95% confidence interval [CI] 1.68-7.35, p = 0.0002). Performing a meta-analysis with previously published data, we found that in a combined sample of 1,256 patients and 1,347 controls from France and Belgium, the OR was 2.81 (95% CI 1.89-4.20, p = 3.60 × 10(-7)).
CONCLUSIONS: These results confirm that ABCA7 LOF variants are enriched in patients with AD and extend this finding to predicted damaging missense variants.
© 2016 American Academy of Neurology.

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Year:  2016        PMID: 27037229      PMCID: PMC4898320          DOI: 10.1212/WNL.0000000000002627

Source DB:  PubMed          Journal:  Neurology        ISSN: 0028-3878            Impact factor:   9.910


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