Literature DB >> 25444012

The National Spina Bifida Patient Registry: profile of a large cohort of participants from the first 10 clinics.

Kathleen J Sawin1, Tiebin Liu2, Elisabeth Ward3, Judy Thibadeau4, Michael S Schechter5, Minn M Soe6, William Walker6.   

Abstract

OBJECTIVE: To use data from the US National Spina Bifida Patient Registry (NSBPR) to describe variations in Contexts of Care, Processes of Care, and Health Outcomes among individuals with spina bifida (SB) receiving care in 10 clinics. STUDY
DESIGN: Reported here are baseline cross-sectional data representing the first visit of 2172 participants from 10 specialized, multidisciplinary SB clinics participating in the NSBPR. We used descriptive statistics, the Fisher exact test, χ(2) test, and Wilcoxon rank-sum test to examine the data.
RESULTS: The mean age was 10.1 (SD 8.1) years with slightly more female subjects (52.5%). The majority was white (63.4%) and relied upon public insurance (53.5%). One-third had sacral lesions, 44.8% had mid-low lumbar lesions, and 24.9% had high lumbar and thoracic lesions. The most common surgery was ventricular shunt placement (65.7%). The most common bladder-management technique among those with bladder impairment was intermittent catheterization (69.0%). Almost 14% experienced a pressure ulcer in the last year. Of those ages 5 years or older with bowel or bladder impairments, almost 30% were continent of stool; a similar percentage was continent of urine. Most variables were associated with type of SB diagnosis.
CONCLUSION: The NSBPR provides a cross section of a predominantly pediatric population of patients followed in specialized SB programs. There were wide variations in the variables studied and major differences in Context of Care, Processes of Care, and Health Outcomes by type of SB. Such wide variation and the differences by type of SB should be considered in future analyses of outcomes.
Copyright © 2015 Elsevier Inc. All rights reserved.

Entities:  

Mesh:

Year:  2014        PMID: 25444012      PMCID: PMC4535790          DOI: 10.1016/j.jpeds.2014.09.039

Source DB:  PubMed          Journal:  J Pediatr        ISSN: 0022-3476            Impact factor:   4.406


  12 in total

1.  Spina bifida outcome: a 25-year prospective.

Authors:  R M Bowman; D G McLone; J A Grant; T Tomita; J A Ito
Journal:  Pediatr Neurosurg       Date:  2001-03       Impact factor: 1.162

2.  Spina bifida subtypes and sub-phenotypes by maternal race/ethnicity in the National Birth Defects Prevention Study.

Authors:  A J Agopian; Mark A Canfield; Richard S Olney; Philip J Lupo; Tunu Ramadhani; Laura E Mitchell; Gary M Shaw; Cynthia A Moore
Journal:  Am J Med Genet A       Date:  2011-12-02       Impact factor: 2.802

3.  Updated National Birth Prevalence estimates for selected birth defects in the United States, 2004-2006.

Authors:  Samantha E Parker; Cara T Mai; Mark A Canfield; Russel Rickard; Ying Wang; Robert E Meyer; Patrick Anderson; Craig A Mason; Julianne S Collins; Russell S Kirby; Adolfo Correa
Journal:  Birth Defects Res A Clin Mol Teratol       Date:  2010-09-28

4.  Patient registry analyses: seize the data, but caveat lector.

Authors:  Michael S Schechter
Journal:  J Pediatr       Date:  2008-12       Impact factor: 4.406

5.  Trends in the postfortification prevalence of spina bifida and anencephaly in the United States.

Authors:  Sheree L Boulet; Quanhe Yang; Cara Mai; Russell S Kirby; Julianne S Collins; James M Robbins; Robert Meyer; Mark A Canfield; Joe Mulinare
Journal:  Birth Defects Res A Clin Mol Teratol       Date:  2008-07

6.  Modelling fortification of corn masa flour with folic acid and the potential impact on Mexican-American women with lower acculturation.

Authors:  Heather C Hamner; Sarah C Tinker; Alina L Flores; Joe Mulinare; Aliki P Weakland; Nicole F Dowling
Journal:  Public Health Nutr       Date:  2012-11-01       Impact factor: 4.022

7.  Proportion of neural tube defects attributable to known risk factors.

Authors:  A J Agopian; Sarah C Tinker; Philip J Lupo; Mark A Canfield; Laura E Mitchell
Journal:  Birth Defects Res A Clin Mol Teratol       Date:  2013-01

Review 8.  Adolescents with a chronic condition: challenges living, challenges treating.

Authors:  Susan M Sawyer; Sarah Drew; Michele S Yeo; Maria T Britto
Journal:  Lancet       Date:  2007-04-28       Impact factor: 79.321

9.  Racial/ethnic differences in the birth prevalence of spina bifida - United States, 1995-2005.

Authors: 
Journal:  MMWR Morb Mortal Wkly Rep       Date:  2009-01-09       Impact factor: 17.586

10.  Testing the feasibility of a National Spina Bifida Patient Registry.

Authors:  Judy K Thibadeau; Elisabeth A Ward; Minn M Soe; Tiebin Liu; Mark Swanson; Kathleen J Sawin; Kurt A Freeman; Heidi Castillo; Karen Rauen; Michael S Schechter
Journal:  Birth Defects Res A Clin Mol Teratol       Date:  2012-11-02
View more
  33 in total

1.  Challenges in pediatric urologic practice: a lifelong view.

Authors:  John S Wiener; Nina Huck; Anne-Sophie Blais; Mandy Rickard; Armando Lorenzo; Heather N McCaffrey Di Carlo; Margaret G Mueller; Raimund Stein
Journal:  World J Urol       Date:  2020-04-23       Impact factor: 4.226

2.  The development of a lifetime care model in comprehensive spina bifida care.

Authors:  Betsy Hopson; Brandon G Rocque; David B Joseph; Danielle Powell; Amie B Jackson McLain; Richard D Davis; Tracey S Wilson; Michael J Conklin; Jeffrey P Blount
Journal:  J Pediatr Rehabil Med       Date:  2018

3.  Correlation Between Neurologic Impairment Grade and Ambulation Status in the Adult Spina Bifida Population.

Authors:  Anne C Tita; John R Frampton; Christian Roehmer; Sara E Izzo; Amy J Houtrow; Brad E Dicianno
Journal:  Am J Phys Med Rehabil       Date:  2019-12       Impact factor: 2.159

Review 4.  Obesity Prevention for Individuals with Spina Bifida.

Authors:  Michele Polfuss; Linda G Bandini; Kathleen J Sawin
Journal:  Curr Obes Rep       Date:  2017-06

5.  The Evolution of Spina Bifida Treatment Through a Biomedical Ethics Lens.

Authors:  Tal Levin-Decanini; Amy Houtrow; Aviva Katz
Journal:  HEC Forum       Date:  2017-09

6.  Longitudinal Study of Bladder Continence in Patients with Spina Bifida in the National Spina Bifida Patient Registry.

Authors:  Tiebin Liu; Lijing Ouyang; Judy Thibadeau; John S Wiener; Jonathan C Routh; Heidi Castillo; Jonathan Castillo; Kurt A Freeman; Kathleen J Sawin; Kathryn Smith; Alexander Van Speybroeck; Rodolfo Valdez
Journal:  J Urol       Date:  2017-11-11       Impact factor: 7.450

7.  Variation in surgical management of neurogenic bowel among centers participating in National Spina Bifida Patient Registry.

Authors:  Jonathan C Routh; David B Joseph; Tiebin Liu; Michael S Schechter; Judy K Thibadeau; M Chad Wallis; Elisabeth A Ward; John S Wiener
Journal:  J Pediatr Rehabil Med       Date:  2017-12-11

Review 8.  Genetic epidemiology of neural tube defects.

Authors:  Philip J Lupo; A J Agopian; Heidi Castillo; Jonathan Castillo; Gerald H Clayton; Nienke P Dosa; Betsy Hopson; David B Joseph; Brandon G Rocque; William O Walker; John S Wiener; Laura E Mitchell
Journal:  J Pediatr Rehabil Med       Date:  2017-12-11

9.  The National Spina Bifida Patient Registry: Past, present, and future.

Authors:  Judy Thibadeau
Journal:  J Pediatr Rehabil Med       Date:  2017-12-11

10.  Urologic provider experiences in transitioning spina bifida patients from pediatric to adult care.

Authors:  Shree Agrawal; Kimberly Slocombe; Tracey Wilson; Stephanie Kielb; Hadley M Wood
Journal:  World J Urol       Date:  2019-01-16       Impact factor: 4.226

View more

北京卡尤迪生物科技股份有限公司 © 2022-2023.