Literature DB >> 23125114

Testing the feasibility of a National Spina Bifida Patient Registry.

Judy K Thibadeau1, Elisabeth A Ward, Minn M Soe, Tiebin Liu, Mark Swanson, Kathleen J Sawin, Kurt A Freeman, Heidi Castillo, Karen Rauen, Michael S Schechter.   

Abstract

BACKGROUND: The purpose of this study was to describe the development and early implementation of a national spina bifida (SB) patient registry, the goal of which is to monitor the health status, clinical care, and outcomes of people with SB by collecting and analyzing patient data from comprehensive SB clinics.
METHODS: Using a web-based, SB-specific electronic medical record, 10 SB clinics collected health-related information for patients diagnosed with myelomeningocele, lipomyelomeningocele, fatty filum, or meningocele. This information was compiled and de-identified for transmission to the Centers for Disease Control and Prevention (CDC) for quality control and analysis.
RESULTS: A total of 2070 patients were enrolled from 2009 through 2011: 84.9% were younger than 18 years of age; 1095 were women; 64.2% were non-Hispanic white; 6.5% were non-Hispanic black or African American; and 24.2% were Hispanic or Latino. Myelomeningocele was the most common diagnosis (81.5%).
CONCLUSIONS: The creation of a National Spina Bifida Patient Registry partnership between the CDC and SB clinics has been feasible. Through planned longitudinal data collection and the inclusion of additional clinics, the data generated by the registry will become more robust and representative of the population of patients attending SB clinics in the United States and will allow for the investigation of patient outcomes.
Copyright © 2012 Wiley Periodicals, Inc.

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Mesh:

Year:  2012        PMID: 23125114      PMCID: PMC4470391          DOI: 10.1002/bdra.23094

Source DB:  PubMed          Journal:  Birth Defects Res A Clin Mol Teratol        ISSN: 1542-0752


  11 in total

Review 1.  Defining and improving data quality in medical registries: a literature review, case study, and generic framework.

Authors:  Danielle G T Arts; Nicolette F De Keizer; Gert-Jan Scheffer
Journal:  J Am Med Inform Assoc       Date:  2002 Nov-Dec       Impact factor: 4.497

2.  Spina bifida outcome: a 25-year prospective.

Authors:  R M Bowman; D G McLone; J A Grant; T Tomita; J A Ito
Journal:  Pediatr Neurosurg       Date:  2001-03       Impact factor: 1.162

3.  Patient registry analyses: seize the data, but caveat lector.

Authors:  Michael S Schechter
Journal:  J Pediatr       Date:  2008-12       Impact factor: 4.406

Review 4.  Advances in growth hormone therapy: a new registry tool.

Authors:  M Pugeat
Journal:  Horm Res       Date:  2004

5.  Epidemiologic study of cystic fibrosis: design and implementation of a prospective, multicenter, observational study of patients with cystic fibrosis in the U.S. and Canada.

Authors:  W J Morgan; S M Butler; C A Johnson; A A Colin; S C FitzSimmons; D E Geller; M W Konstan; M J Light; H R Rabin; W E Regelmann; D V Schidlow; D C Stokes; M E Wohl; H Kaplowitz; M M Wyatt; S Stryker
Journal:  Pediatr Pulmonol       Date:  1999-10

6.  Longevity of patients born with myelomeningocele.

Authors:  C M Dillon; B E Davis; S Duguay; K D Seidel; D B Shurtleff
Journal:  Eur J Pediatr Surg       Date:  2000-12       Impact factor: 2.191

Review 7.  The cystic fibrosis therapeutics development network (CF TDN): a paradigm of a clinical trials network for genetic and orphan diseases.

Authors:  C H Goss; N Mayer-Hamblett; R A Kronmal; B W Ramsey
Journal:  Adv Drug Deliv Rev       Date:  2002-12-05       Impact factor: 15.470

8.  The cost of preventable conditions in adults with spina bifida.

Authors:  S L Kinsman; M C Doehring
Journal:  Eur J Pediatr Surg       Date:  1996-12       Impact factor: 2.191

9.  Pompe disease: design, methodology, and early findings from the Pompe Registry.

Authors:  Barry J Byrne; Priya S Kishnani; Laura E Case; Luciano Merlini; Wolfgang Müller-Felber; Suyash Prasad; Ans van der Ploeg
Journal:  Mol Genet Metab       Date:  2011-02-11       Impact factor: 4.797

10.  Disbanding a multidisciplinary clinic: effects on the health care of myelomeningocele patients.

Authors:  B A Kaufman; A Terbrock; N Winters; J Ito; A Klosterman; T S Park
Journal:  Pediatr Neurosurg       Date:  1994       Impact factor: 1.162

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  27 in total

1.  Skin breakdown of the feet in patients with spina bifida: Analysis of risk factors.

Authors:  Michael J Conklin; Betsy Hopson; Anastasia Arynchyna; Travis Atchley; Courtney Trapp; Brandon G Rocque
Journal:  J Pediatr Rehabil Med       Date:  2018

2.  The development of a lifetime care model in comprehensive spina bifida care.

Authors:  Betsy Hopson; Brandon G Rocque; David B Joseph; Danielle Powell; Amie B Jackson McLain; Richard D Davis; Tracey S Wilson; Michael J Conklin; Jeffrey P Blount
Journal:  J Pediatr Rehabil Med       Date:  2018

3.  Longitudinal Study of Bladder Continence in Patients with Spina Bifida in the National Spina Bifida Patient Registry.

Authors:  Tiebin Liu; Lijing Ouyang; Judy Thibadeau; John S Wiener; Jonathan C Routh; Heidi Castillo; Jonathan Castillo; Kurt A Freeman; Kathleen J Sawin; Kathryn Smith; Alexander Van Speybroeck; Rodolfo Valdez
Journal:  J Urol       Date:  2017-11-11       Impact factor: 7.450

4.  Factors Associated with Mobility Outcomes in a National Spina Bifida Patient Registry.

Authors:  Brad E Dicianno; Amol Karmarkar; Amy Houtrow; Theresa M Crytzer; Katelyn M Cushanick; Andrew McCoy; Pamela Wilson; James Chinarian; Jacob Neufeld; Kathryn Smith; Diane M Collins
Journal:  Am J Phys Med Rehabil       Date:  2015-12       Impact factor: 2.159

5.  Sociodemographic attributes and spina bifida outcomes.

Authors:  Michael S Schechter; Tiebin Liu; Minn Soe; Mark Swanson; Elisabeth Ward; Judy Thibadeau
Journal:  Pediatrics       Date:  2015-03-16       Impact factor: 7.124

6.  Variation in surgical management of neurogenic bowel among centers participating in National Spina Bifida Patient Registry.

Authors:  Jonathan C Routh; David B Joseph; Tiebin Liu; Michael S Schechter; Judy K Thibadeau; M Chad Wallis; Elisabeth A Ward; John S Wiener
Journal:  J Pediatr Rehabil Med       Date:  2017-12-11

7.  The National Spina Bifida Patient Registry: Past, present, and future.

Authors:  Judy Thibadeau
Journal:  J Pediatr Rehabil Med       Date:  2017-12-11

8.  Variation in bowel and bladder continence across US spina bifida programs: A descriptive study.

Authors:  Kurt A Freeman; Heidi Castillo; Jonathan Castillo; Tiebin Liu; Michael Schechter; John S Wiener; Judy Thibadeau; Elisabeth Ward; Timothy Brei
Journal:  J Pediatr Rehabil Med       Date:  2017-12-11

9.  Bowel management and continence in adults with spina bifida: Results from the National Spina Bifida Patient Registry 2009-15.

Authors:  John S Wiener; Kristina D Suson; Jonathan Castillo; Jonathan C Routh; Stacy Tanaka; Tiebin Liu; Elisabeth Ward; Judy Thibadeau; David Joseph; National Spina Bifida Patient Registry
Journal:  J Pediatr Rehabil Med       Date:  2017-12-11

10.  Differences in continence rates in individuals with spina bifida based on ethnicity.

Authors:  Kathryn A Smith; Tiebin Liu; Kurt A Freeman; Cecily Betz; Gerald H Clayton; Heidi Castillo; Jonathan Castillo; Duong Tu; Alexander Van Speybroeck; William O Walker
Journal:  J Pediatr Rehabil Med       Date:  2019
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