Literature DB >> 20647559

Therapeutic potential of valproic acid for retinitis pigmentosa.

C M Clemson1, R Tzekov, M Krebs, J M Checchi, C Bigelow, S Kaushal.   

Abstract

BACKGROUND/AIM: To examine the efficacy and safety of valproic acid (VPA) in patients with retinitis pigmentosa (RP).
METHODS: Thirteen eyes were examined before and after brief treatment (average 4 months) with VPA. Visual fields (VF) for each eye were defined using digitised Goldmann Kinetic Perimetry tracings. VF areas were log-transformed and VF loss/gain relative to baseline was calculated. Visual acuity was measured using a Snellen chart at a distance of 20 feet (6.1 m). Values were converted to the logarithm of the minimum angle of resolution (logMAR) score.
RESULTS: Nine eyes had improved VF with treatment, two eyes had decreased VF and two eyes experienced no change, with an overall average increase of 11%. Assuming typical loss in VF area without treatment, this increase in VF was statistically significant (p<0.02). An average decrease (0.172) in the logMAR scores was seen in these 13 eyes, which translates to a positive change in Snellen score of approximately 20/47 to 20/32, which was significant (p<0.02) assuming no loss in acuity without treatment. Side effects were mild and well tolerated.
CONCLUSION: Treatment with VPA is suggestive of a therapeutic benefit to patients with RP. A placebo-controlled clinical trial will be necessary to assess the efficacy and safety of VPA for RP rigorously.

Entities:  

Mesh:

Substances:

Year:  2010        PMID: 20647559     DOI: 10.1136/bjo.2009.175356

Source DB:  PubMed          Journal:  Br J Ophthalmol        ISSN: 0007-1161            Impact factor:   4.638


  41 in total

Review 1.  Therapeutic Approaches to Histone Reprogramming in Retinal Degeneration.

Authors:  Andre K Berner; Mark E Kleinman
Journal:  Adv Exp Med Biol       Date:  2016       Impact factor: 2.622

Review 2.  Learning to see again: biological constraints on cortical plasticity and the implications for sight restoration technologies.

Authors:  Michael Beyeler; Ariel Rokem; Geoffrey M Boynton; Ione Fine
Journal:  J Neural Eng       Date:  2017-06-14       Impact factor: 5.379

3.  Variability and Errors of Manually Digitized Goldmann Visual Fields.

Authors:  Michael P Barry; Ava K Bittner; Liancheng Yang; Rebecca Marcus; Mian Haris Iftikhar; Gislin Dagnelie
Journal:  Optom Vis Sci       Date:  2016-07       Impact factor: 1.973

Review 4.  Protein misfolding and retinal degeneration.

Authors:  Radouil Tzekov; Linda Stein; Shalesh Kaushal
Journal:  Cold Spring Harb Perspect Biol       Date:  2011-11-01       Impact factor: 10.005

5.  Valproic Acid for a Treatment of Retinitis Pigmentosa: Reasons for Optimism and Caution.

Authors:  Levi Todd; Christopher Zelinka
Journal:  J Neurosci       Date:  2017-05-24       Impact factor: 6.167

6.  Epigenetic regulation of retinal development and disease.

Authors:  Rajesh C Rao; Anne K Hennig; Muhammad T A Malik; Dong Feng Chen; Shiming Chen
Journal:  J Ocul Biol Dis Infor       Date:  2012-03-29

7.  Opposing Effects of Valproic Acid Treatment Mediated by Histone Deacetylase Inhibitor Activity in Four Transgenic X. laevis Models of Retinitis Pigmentosa.

Authors:  Ruanne Y J Vent-Schmidt; Runxia H Wen; Zusheng Zong; Colette N Chiu; Beatrice M Tam; Christopher G May; Orson L Moritz
Journal:  J Neurosci       Date:  2017-01-25       Impact factor: 6.167

8.  Effect of Oral Valproic Acid vs Placebo for Vision Loss in Patients With Autosomal Dominant Retinitis Pigmentosa: A Randomized Phase 2 Multicenter Placebo-Controlled Clinical Trial.

Authors:  David G Birch; Paul S Bernstein; Alessandro Iannacone; Mark E Pennesi; Byron L Lam; John Heckenlively; Karl Csaky; Mary Elizabeth Hartnett; Kevin L Winthrop; Thiran Jayasundera; Dianna K Hughbanks-Wheaton; Judith Warner; Paul Yang; Gary Edd Fish; Michael P Teske; Neal L Sklaver; Laura Erker; Elvira Chegarnov; Travis Smith; Aimee Wahle; Paul C VanVeldhuisen; Jennifer McCormack; Robert Lindblad; Steven Bramer; Stephen Rose; Patricia Zilliox; Peter J Francis; Richard G Weleber
Journal:  JAMA Ophthalmol       Date:  2018-08-01       Impact factor: 7.389

Review 9.  The molecular and cellular basis of rhodopsin retinitis pigmentosa reveals potential strategies for therapy.

Authors:  Dimitra Athanasiou; Monica Aguila; James Bellingham; Wenwen Li; Caroline McCulley; Philip J Reeves; Michael E Cheetham
Journal:  Prog Retin Eye Res       Date:  2017-10-16       Impact factor: 21.198

10.  Proteasome overload is a common stress factor in multiple forms of inherited retinal degeneration.

Authors:  Ekaterina S Lobanova; Stella Finkelstein; Nikolai P Skiba; Vadim Y Arshavsky
Journal:  Proc Natl Acad Sci U S A       Date:  2013-05-28       Impact factor: 11.205

View more

北京卡尤迪生物科技股份有限公司 © 2022-2023.