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Literature DB >> 9927490

The genesis of cystic fibrosis lung disease.

J J Wine¹.

Abstract

Entities: Disease

Mesh：

Substances：

Year: 1999 PMID： 9927490 PMCID： PMC407906 DOI： 10.1172/JCI6222

Source DB: PubMed Journal: J Clin Invest ISSN： 0021-9738 Impact factor: 14.808

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27 in total

1. Simple technique for culture of highly differentiated cells from dog tracheal epithelium.

Authors: M Kondo; W E Finkbeiner; J H Widdicombe
Journal: Am J Physiol Date: 1991-08

2. Missing Cl conductance in cystic fibrosis.

Authors: P M Quinton
Journal: Am J Physiol Date: 1986-10

3. Expression of the cystic fibrosis gene in adult human lung.

Authors: J F Engelhardt; M Zepeda; J A Cohn; J R Yankaskas; J M Wilson
Journal: J Clin Invest Date: 1994-02 Impact factor: 14.808

4. Defective regulation of outwardly rectifying Cl- channels by protein kinase A corrected by insertion of CFTR.

Authors: M Egan; T Flotte; S Afione; R Solow; P L Zeitlin; B J Carter; W B Guggino
Journal: Nature Date: 1992-08-13 Impact factor: 49.962

5. Chloride impermeability in cystic fibrosis.

Authors: P M Quinton
Journal: Nature Date: 1983-02-03 Impact factor: 49.962

6. Mislocalization of delta F508 CFTR in cystic fibrosis sweat gland.

Authors: N Kartner; O Augustinas; T J Jensen; A L Naismith; J R Riordan
Journal: Nat Genet Date: 1992-08 Impact factor: 38.330

7. Submucosal glands are the predominant site of CFTR expression in the human bronchus.

Authors: J F Engelhardt; J R Yankaskas; S A Ernst; Y Yang; C R Marino; R C Boucher; J A Cohn; J M Wilson
Journal: Nat Genet Date: 1992-11 Impact factor: 38.330

8. Calu-3: a human airway epithelial cell line that shows cAMP-dependent Cl- secretion.

Authors: B Q Shen; W E Finkbeiner; J J Wine; R J Mrsny; J H Widdicombe
Journal: Am J Physiol Date: 1994-05

9. Hyperabsorption of Na+ and raised Ca(2+)-mediated Cl- secretion in nasal epithelia of CF mice.

Authors: B R Grubb; R N Vick; R C Boucher
Journal: Am J Physiol Date: 1994-05

10. Abnormal ion permeation through cystic fibrosis respiratory epithelium.

Authors: M R Knowles; M J Stutts; A Spock; N Fischer; J T Gatzy; R C Boucher
Journal: Science Date: 1983-09-09 Impact factor: 47.728

67 in total

Review 1. Airway plumbing.

Authors: J W Hanrahan
Journal: J Clin Invest Date: 2000-05 Impact factor: 14.808

The genesis of cystic fibrosis lung disease.

1. Simple technique for culture of highly differentiated cells from dog tracheal epithelium.

2. Missing Cl conductance in cystic fibrosis.

3. Expression of the cystic fibrosis gene in adult human lung.

4. Defective regulation of outwardly rectifying Cl- channels by protein kinase A corrected by insertion of CFTR.

5. Chloride impermeability in cystic fibrosis.

6. Mislocalization of delta F508 CFTR in cystic fibrosis sweat gland.

7. Submucosal glands are the predominant site of CFTR expression in the human bronchus.

8. Calu-3: a human airway epithelial cell line that shows cAMP-dependent Cl- secretion.

9. Hyperabsorption of Na+ and raised Ca(2+)-mediated Cl- secretion in nasal epithelia of CF mice.

10. Abnormal ion permeation through cystic fibrosis respiratory epithelium.

Review 1. Airway plumbing.

Review 2. Status of gene therapy for cystic fibrosis lung disease.

3. Characterization of basolateral K+ channels underlying anion secretion in the human airway cell line Calu-3.

Review 4. Mucus clearance as a primary innate defense mechanism for mammalian airways.

5. Noninvasive in vivo fluorescence measurement of airway-surface liquid depth, salt concentration, and pH.

Review 6. Rescuing protein conformation: prospects for pharmacological therapy in cystic fibrosis.

7. Cystic fibrosis presenting with corneal perforation and crystalline lens extrusion.

Review 8. The role of inflammation in the pathophysiology of CF lung disease.

Review 9. The Evolution of Cystic Fibrosis Care.

Review 10. Targeting sphingosine-1-phosphate signaling in lung diseases.