Literature DB >> 12464661

Rescuing protein conformation: prospects for pharmacological therapy in cystic fibrosis.

Marina S Gelman1, Ron R Kopito.   

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Year:  2002        PMID： 12464661      PMCID： PMC151638          DOI： 10.1172/JCI16786

Source DB:  PubMed          Journal:  J Clin Invest        ISSN： 0021-9738            Impact factor:   14.808


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  56 in total

Review 1.  Pharmacological chaperones: a new twist on receptor folding.

Authors:  J P Morello; U E Petäjä-Repo; D G Bichet; M Bouvier
Journal:  Trends Pharmacol Sci       Date:  2000-12       Impact factor: 14.819

Review 2.  Aggresomes, inclusion bodies and protein aggregation.

Authors:  R R Kopito
Journal:  Trends Cell Biol       Date:  2000-12       Impact factor: 20.808

3.  Dynamic interaction of BiP and ER stress transducers in the unfolded-protein response.

Authors:  A Bertolotti; Y Zhang; L M Hendershot; H P Harding; D Ron
Journal:  Nat Cell Biol       Date:  2000-06       Impact factor: 28.824

4.  Sodium 4-phenylbutyrate downregulates Hsc70: implications for intracellular trafficking of DeltaF508-CFTR.

Authors:  R C Rubenstein; P L Zeitlin
Journal:  Am J Physiol Cell Physiol       Date:  2000-02       Impact factor: 4.249

Review 5.  Pharmacological treatment of the ion transport defect in cystic fibrosis.

Authors:  G M Roomans
Journal:  Expert Opin Investig Drugs       Date:  2001-01       Impact factor: 6.206

Review 6.  Histone deacetylase inhibitors: inducers of differentiation or apoptosis of transformed cells.

Authors:  P A Marks; V M Richon; R A Rifkind
Journal:  J Natl Cancer Inst       Date:  2000-08-02       Impact factor: 13.506

Review 7.  Regulated trafficking of the CFTR chloride channel.

Authors:  B Kleizen; I Braakman; H R de Jonge
Journal:  Eur J Cell Biol       Date:  2000-08       Impact factor: 4.492

8.  The Delta F508 mutation shortens the biochemical half-life of plasma membrane CFTR in polarized epithelial cells.

Authors:  G D Heda; M Tanwani; C R Marino
Journal:  Am J Physiol Cell Physiol       Date:  2001-01       Impact factor: 4.249

9.  Direct block of the cystic fibrosis transmembrane conductance regulator Cl(-) channel by butyrate and phenylbutyrate.

Authors:  P Linsdell
Journal:  Eur J Pharmacol       Date:  2001-01-12       Impact factor: 4.432

10.  Interaction of the immunosuppressant deoxyspergualin with a member of the Hsp70 family of heat shock proteins.

Authors:  S G Nadler; M A Tepper; B Schacter; C E Mazzucco
Journal:  Science       Date:  1992-10-16       Impact factor: 47.728
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  25 in total

1.  The cellular response to aggregated proteins associated with human disease.

Authors:  David H Perlmutter
Journal:  J Clin Invest       Date:  2002-11       Impact factor: 14.808

Review 2.  Alpha1-antitrypsin polymerization and the serpinopathies: pathobiology and prospects for therapy.

Authors:  David A Lomas; Ravi Mahadeva
Journal:  J Clin Invest       Date:  2002-12       Impact factor: 14.808

Review 3.  Orchestrating the unfolded protein response in health and disease.

Authors:  Randal J Kaufman
Journal:  J Clin Invest       Date:  2002-11       Impact factor: 14.808

4.  Adenosine A2A receptor is involved in cell surface expression of A2B receptor.

Authors:  Kengo Moriyama; Michail V Sitkovsky
Journal:  J Biol Chem       Date:  2010-10-06       Impact factor: 5.157

Review 5.  The unfolded protein response in protein aggregating diseases.

Authors:  Alexander Gow; Ramaswamy Sharma
Journal:  Neuromolecular Med       Date:  2003       Impact factor: 3.843

6.  The endoplasmic reticulum-associated degradation is necessary for plant salt tolerance.

Authors:  Lijing Liu; Feng Cui; Qingliang Li; Bojiao Yin; Huawei Zhang; Baoying Lin; Yaorong Wu; Ran Xia; Sanyuan Tang; Qi Xie
Journal:  Cell Res       Date:  2010-12-28       Impact factor: 25.617

Review 7.  Protein processing and inflammatory signaling in Cystic Fibrosis: challenges and therapeutic strategies.

Authors:  C N Belcher; N Vij
Journal:  Curr Mol Med       Date:  2010-02       Impact factor: 2.222

8.  Structure of nucleotide-binding domain 1 of the cystic fibrosis transmembrane conductance regulator.

Authors:  Hal A Lewis; Sean G Buchanan; Stephen K Burley; Kris Conners; Mark Dickey; Michael Dorwart; Richard Fowler; Xia Gao; William B Guggino; Wayne A Hendrickson; John F Hunt; Margaret C Kearins; Don Lorimer; Peter C Maloney; Kai W Post; Kanagalaghatta R Rajashankar; Marc E Rutter; J Michael Sauder; Stephanie Shriver; Patrick H Thibodeau; Philip J Thomas; Marie Zhang; Xun Zhao; Spencer Emtage
Journal:  EMBO J       Date:  2003-12-18       Impact factor: 11.598

9.  Endocytic trafficking routes of wild type and DeltaF508 cystic fibrosis transmembrane conductance regulator.

Authors:  Martina Gentzsch; Xiu-Bao Chang; Liying Cui; Yufeng Wu; Victor V Ozols; Amit Choudhury; Richard E Pagano; John R Riordan
Journal:  Mol Biol Cell       Date:  2004-04-09       Impact factor: 4.138

10.  A striking quality control subcompartment in Saccharomyces cerevisiae: the endoplasmic reticulum-associated compartment.

Authors:  Gregory Huyer; Gaby L Longsworth; Deborah L Mason; Monica P Mallampalli; J Michael McCaffery; Robin L Wright; Susan Michaelis
Journal:  Mol Biol Cell       Date:  2003-12-10       Impact factor: 4.138
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