Literature DB >> 8769508

Is resection of bronchiectasis beneficial in patients with primary ciliary dyskinesia?

H J Smit1, A J Schreurs, J M Van den Bosch, C J Westermann.   

Abstract

A retrospective study of 21 patients with primary ciliary dyskinesia (PCD) was done. Thirteen had prior resection of bronchiectasis and eight had not. Information about present complaints was obtained by a questionnaire. The prevalence of present respiratory symptoms was the same in both groups. The surgical patients had more severe disease and 85% of them considered the operation beneficial. Selected patients with PCD may have improved conditions with resection of bronchiectasis.

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Mesh:

Year:  1996        PMID: 8769508     DOI: 10.1378/chest.109.6.1541

Source DB:  PubMed          Journal:  Chest        ISSN: 0012-3692            Impact factor:   9.410


  14 in total

Review 1.  Primary ciliary dyskinesia, an orphan disease.

Authors:  Mieke Boon; Mark Jorissen; Marijke Proesmans; Kris De Boeck
Journal:  Eur J Pediatr       Date:  2012-07-10       Impact factor: 3.183

Review 2.  Primary ciliary dyskinesia.

Authors:  Jason Lobo; Maimoona A Zariwala; Peadar G Noone
Journal:  Semin Respir Crit Care Med       Date:  2015-03-31       Impact factor: 3.119

3.  Primary Ciliary Dyskinesia (PCD): A genetic disorder of motile cilia.

Authors:  Margaret W Leigh; Amjad Horani; BreAnna Kinghorn; Michael G O'Connor; Maimoona A Zariwala; Michael R Knowles
Journal:  Transl Sci Rare Dis       Date:  2019-07-04

Review 4.  Update of respiratory tract disease in children with primary ciliary dyskinesia.

Authors:  Scott D Sagel; Stephanie D Davis; Paolo Campisi; Sharon D Dell
Journal:  Proc Am Thorac Soc       Date:  2011-09

Review 5.  Primary ciliary dyskinesia. Recent advances in diagnostics, genetics, and characterization of clinical disease.

Authors:  Michael R Knowles; Leigh Anne Daniels; Stephanie D Davis; Maimoona A Zariwala; Margaret W Leigh
Journal:  Am J Respir Crit Care Med       Date:  2013-10-15       Impact factor: 21.405

Review 6.  Primary ciliary dyskinesia: recent advances in pathogenesis, diagnosis and treatment.

Authors:  Hauw Lie; Thomas Ferkol
Journal:  Drugs       Date:  2007       Impact factor: 9.546

Review 7.  Primary Ciliary Dyskinesia.

Authors:  Michael R Knowles; Maimoona Zariwala; Margaret Leigh
Journal:  Clin Chest Med       Date:  2016-06-30       Impact factor: 2.878

Review 8.  Clinical and genetic aspects of primary ciliary dyskinesia/Kartagener syndrome.

Authors:  Margaret W Leigh; Jessica E Pittman; Johnny L Carson; Thomas W Ferkol; Sharon D Dell; Stephanie D Davis; Michael R Knowles; Maimoona A Zariwala
Journal:  Genet Med       Date:  2009-07       Impact factor: 8.822

Review 9.  Diagnosis of primary ciliary dyskinesia.

Authors:  Mary Anne Kowal Olm; Elia Garcia Caldini; Thais Mauad
Journal:  J Bras Pneumol       Date:  2015 May-Jun       Impact factor: 2.624

10.  Genetics, diagnosis, and future treatment strategies for primary ciliary dyskinesia.

Authors:  M Leigh Anne Daniels; Peadar G Noone
Journal:  Expert Opin Orphan Drugs       Date:  2014-11-29       Impact factor: 0.694

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