Literature DB >> 8758135

Uncooked cornstarch--efficacy in type I glycogenosis.

P J Lee1, M A Dixon, J V Leonard.   

Abstract

Uncooked cornstarch (UCCS) loads in 14 patients with type 1 glycogenosis revealed that satisfactory glycaemia was achieved for a median of 4.25 hours (range 2.5 to 6). Length of glycaemia was related weakly to UCCS dose, but not to patient age or measures of metabolic control. Careful monitoring is required during UCCS treatment.

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Year:  1996        PMID： 8758135      PMCID： PMC1511553          DOI： 10.1136/adc.74.6.546

Source DB:  PubMed          Journal:  Arch Dis Child        ISSN： 0003-9888            Impact factor:   3.791


  6 in total

1.  Cornstarch therapy in type I glycogen-storage disease.

Authors:  Y T Chen; M Cornblath; J B Sidbury
Journal:  N Engl J Med       Date:  1984-01-19       Impact factor: 91.245

2.  Disordered intestinal function in glycogen storage disease.

Authors:  P J Milla; D A Atherton; J V Leonard; O H Wolff; B D Lake
Journal:  J Inherit Metab Dis       Date:  1978       Impact factor: 4.982

3.  The dietary treatment of children with type I glycogen storage disease with slow release carbohydrate.

Authors:  G P Smit; R Berger; R Potasnick; S W Moses; J Fernandes
Journal:  Pediatr Res       Date:  1984-09       Impact factor: 3.756

4.  Glycemic index of foods: a physiological basis for carbohydrate exchange.

Authors:  D J Jenkins; T M Wolever; R H Taylor; H Barker; H Fielden; J M Baldwin; A C Bowling; H C Newman; A L Jenkins; D V Goff
Journal:  Am J Clin Nutr       Date:  1981-03       Impact factor: 7.045

5.  Development of functional responses in human exocrine pancreas.

Authors:  E Lebenthal; P C Lee
Journal:  Pediatrics       Date:  1980-10       Impact factor: 7.124

Review 6.  Nutrition therapy for hepatic glycogen storage diseases.

Authors:  T Goldberg; A E Slonim
Journal:  J Am Diet Assoc       Date:  1993-12
  6 in total
  7 in total

1.  Continuous glucose monitoring in children with glycogen storage disease type I.

Authors:  E Hershkovitz; A Rachmel; H Ben-Zaken; M Phillip
Journal:  J Inherit Metab Dis       Date:  2001-12       Impact factor: 4.982

2.  Successful long-term treatment of hepatic carnitine palmitoyltransferase I deficiency and a novel mutation.

Authors:  J M Stoler; M A Sabry; C Hanley; C L Hoppel; V E Shih
Journal:  J Inherit Metab Dis       Date:  2004       Impact factor: 4.982

3.  Development of minimally invasive 13C-glucose breath test to examine different exogenous carbohydrate sources in patients with glycogen storage disease type Ia.

Authors:  Abrar Turki; Sylvia Stockler; Sandra Sirrs; Ramona Salvarinova; Gloria Ho; Jennifer Branov; Annie Rosen-Heath; Taryn Bosdet; Rajavel Elango
Journal:  Mol Genet Metab Rep       Date:  2022-05-11

Review 4.  Glycogen storage diseases: new perspectives.

Authors:  Hasan Ozen
Journal:  World J Gastroenterol       Date:  2007-05-14       Impact factor: 5.742

5.  A novel starch for the treatment of glycogen storage diseases.

Authors:  K Bhattacharya; R C Orton; X Qi; H Mundy; D W Morley; M P Champion; S Eaton; R F Tester; P J Lee
Journal:  J Inherit Metab Dis       Date:  2007-05-19       Impact factor: 4.982

Review 6.  Investigation and management of the hepatic glycogen storage diseases.

Authors:  Kaustuv Bhattacharya
Journal:  Transl Pediatr       Date:  2015-07

7.  In vitro digestion of starches in a dynamic gastrointestinal model: an innovative study to optimize dietary management of patients with hepatic glycogen storage diseases.

Authors:  Tatiéle Nalin; Koen Venema; David A Weinstein; Carolina F M de Souza; Ingrid D S Perry; Mario T R van Wandelen; Margreet van Rijn; G Peter A Smit; Ida V D Schwartz; Terry G J Derks
Journal:  J Inherit Metab Dis       Date:  2014-09-16       Impact factor: 4.982
  7 in total

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