Literature DB >> 8411992

Reduced phospholipase activity, peptide storage and the pathogenesis of canine neuronal ceroid-lipofuscinosis.

G Dawson1, J Kilkus, A N Siakotos.   

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Year:  1993        PMID: 8411992     DOI: 10.1007/bf00710276

Source DB:  PubMed          Journal:  J Inherit Metab Dis        ISSN: 0141-8955            Impact factor:   4.982


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  14 in total

Review 1.  Ubiquitin-mediated protein degradation.

Authors:  A Hershko
Journal:  J Biol Chem       Date:  1988-10-25       Impact factor: 5.157

2.  Tricine-sodium dodecyl sulfate-polyacrylamide gel electrophoresis for the separation of proteins in the range from 1 to 100 kDa.

Authors:  H Schägger; G von Jagow
Journal:  Anal Biochem       Date:  1987-11-01       Impact factor: 3.365

Review 3.  Storage bodies in the ceroid-lipofuscinoses (Batten disease): low-molecular-weight components, unusual amino acids and reconstitution of fluorescent bodies from non-fluorescent components.

Authors:  D N Palmer; S L Bayliss; P A Clifton; V J Grant
Journal:  J Inherit Metab Dis       Date:  1993       Impact factor: 4.982

4.  Purification of lysosomal phospholipase A and demonstration of proteins that inhibit phospholipase A in a lysosomal fraction from rat kidney cortex.

Authors:  K Y Hostetler; M F Gardner; J R Giordano
Journal:  Biochemistry       Date:  1986-10-21       Impact factor: 3.162

5.  Evidence for two distinct forms of mammalian beta-mannosidase.

Authors:  G Dawson
Journal:  J Biol Chem       Date:  1982-04-10       Impact factor: 5.157

6.  Mitochondrial ATP synthase subunit c storage in the ceroid-lipofuscinoses (Batten disease).

Authors:  D N Palmer; I M Fearnley; J E Walker; N A Hall; B D Lake; L S Wolfe; M Haltia; R D Martinus; R D Jolly
Journal:  Am J Med Genet       Date:  1992-02-15

7.  4-Hydroxynonenal: a specific indicator for canine neuronal-retinal ceroidosis.

Authors:  A N Siakotos; R Bray; E Dratz; F van Kuijk; A Sevanian; N Koppang
Journal:  Am J Med Genet Suppl       Date:  1988

8.  Ovine ceroid lipofuscinosis. The major lipopigment protein and the lipid-binding subunit of mitochondrial ATP synthase have the same NH2-terminal sequence.

Authors:  D N Palmer; R D Martinus; S M Cooper; G G Midwinter; J C Reid; R D Jolly
Journal:  J Biol Chem       Date:  1989-04-05       Impact factor: 5.157

9.  Phospholipases and the molecular basis for the formation of ceroid in Batten disease.

Authors:  G Dawson; S A Dawson; A N Siakotos
Journal:  Adv Exp Med Biol       Date:  1989       Impact factor: 2.622

10.  The large-scale separation of peroxisomes, mitochondria, and lysosomes from the livers of rats injected with triton WR-1339. Improved isolation procedures, automated analysis, biochemical and morphological properties of fractions.

Authors:  F Leighton; B Poole; H Beaufay; P Baudhuin; J W Coffey; S Fowler; C De Duve
Journal:  J Cell Biol       Date:  1968-05       Impact factor: 10.539

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