Literature DB >> 8411984

Storage bodies in the ceroid-lipofuscinoses (Batten disease): low-molecular-weight components, unusual amino acids and reconstitution of fluorescent bodies from non-fluorescent components.

D N Palmer1, S L Bayliss, P A Clifton, V J Grant.   

Abstract

Entities:  

Mesh：

Substances：

Year:  1993        PMID： 8411984     DOI： 10.1007/bf00710268

Source DB:  PubMed          Journal:  J Inherit Metab Dis        ISSN： 0141-8955            Impact factor:   4.982


× No keyword cloud information.
  11 in total

1.  The sequence of the major protein stored in ovine ceroid lipofuscinosis is identical with that of the dicyclohexylcarbodiimide-reactive proteolipid of mitochondrial ATP synthase.

Authors:  I M Fearnley; J E Walker; R D Martinus; R D Jolly; K B Kirkland; G J Shaw; D N Palmer
Journal:  Biochem J       Date:  1990-06-15       Impact factor: 3.857

2.  Tricine-sodium dodecyl sulfate-polyacrylamide gel electrophoresis for the separation of proteins in the range from 1 to 100 kDa.

Authors:  H Schägger; G von Jagow
Journal:  Anal Biochem       Date:  1987-11-01       Impact factor: 3.365

Review 3.  Lysosomal storage of the DCCD reactive proteolipid subunit of mitochondrial ATP synthase in human and ovine ceroid lipofuscinoses.

Authors:  D N Palmer; I M Fearnley; S M Medd; J E Walker; R D Martinus; S L Bayliss; N A Hall; B D Lake; L S Wolfe; R D Jolly
Journal:  Adv Exp Med Biol       Date:  1989       Impact factor: 2.622

4.  Low molecular weight urinary peptides in ceroid-lipofuscinoses: potential biochemical markers for the juvenile subtype.

Authors:  G U LaBadie; R K Pullarkat
Journal:  Am J Med Genet       Date:  1990-12

5.  Methylated lysine in storage body protein of sheep with hereditary ceroid-lipofuscinosis.

Authors:  M L Katz; K O Gerhardt
Journal:  Biochim Biophys Acta       Date:  1992-02-14

Review 6.  Sheep and other animals with ceroid-lipofuscinoses: their relevance to Batten disease.

Authors:  R D Jolly; R D Martinus; D N Palmer
Journal:  Am J Med Genet       Date:  1992-02-15

7.  Mitochondrial ATP synthase subunit c storage in the ceroid-lipofuscinoses (Batten disease).

Authors:  D N Palmer; I M Fearnley; J E Walker; N A Hall; B D Lake; L S Wolfe; M Haltia; R D Martinus; R D Jolly
Journal:  Am J Med Genet       Date:  1992-02-15

8.  Ceroid lipofuscinosis in sheep. I. Bis(monoacylglycero)phosphate, dolichol, ubiquinone, phospholipids, fatty acids, and fluorescence in liver lipopigment lipids.

Authors:  D N Palmer; D R Husbands; P J Winter; J W Blunt; R D Jolly
Journal:  J Biol Chem       Date:  1986-02-05       Impact factor: 5.157

9.  Ovine ceroid lipofuscinosis. The major lipopigment protein and the lipid-binding subunit of mitochondrial ATP synthase have the same NH2-terminal sequence.

Authors:  D N Palmer; R D Martinus; S M Cooper; G G Midwinter; J C Reid; R D Jolly
Journal:  J Biol Chem       Date:  1989-04-05       Impact factor: 5.157

10.  Storage protein in hereditary ceroid-lipofuscinosis contains S-methylated methionine.

Authors:  M L Katz; K O Gerhardt
Journal:  Mech Ageing Dev       Date:  1990-04-30       Impact factor: 5.432
View more
  3 in total

1.  Reduced phospholipase activity, peptide storage and the pathogenesis of canine neuronal ceroid-lipofuscinosis.

Authors:  G Dawson; J Kilkus; A N Siakotos
Journal:  J Inherit Metab Dis       Date:  1993       Impact factor: 4.982

Review 2.  Ceroid, lipofuscin and the ceroid-lipofuscinoses (Batten disease).

Authors:  R D Jolly; R R Dalefield; D N Palmer
Journal:  J Inherit Metab Dis       Date:  1993       Impact factor: 4.982

3.  Mitochondrial ATP synthase subunit c stored in hereditary ceroid-lipofuscinosis contains trimethyl-lysine.

Authors:  M L Katz; C L Gao; J A Tompkins; R T Bronson; D T Chin
Journal:  Biochem J       Date:  1995-09-15       Impact factor: 3.857
  3 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.