Literature DB >> 8176563

Hypocomplementemic urticarial vasculitis syndrome with severe systemic manifestations.

A Martini1, A Ravelli, S Albani, F De Benedetti, M Massa, J J Wisnieski.   

Abstract

We describe two children with clinical and laboratory features of hypocomplementemic urticarial vasculitis syndrome. Both patients had severe, life-threatening manifestations: rapidly progressive glomerulonephritis (patient 1) and pulmonary hemorrhage (patient 2). We conclude that this syndrome may be a potentially severe multisystem disease.

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Year:  1994        PMID: 8176563     DOI: 10.1016/s0022-3476(05)81367-8

Source DB:  PubMed          Journal:  J Pediatr        ISSN: 0022-3476            Impact factor:   4.406


  7 in total

1.  Hypocomplementemic urticarial vasculitis (HUVS) with precocious emphysema responsive to azathioprine.

Authors:  L Breda; M Nozzi; S Harari; M Del Torto; M Lucantoni; A Scardapane; F Chiarelli
Journal:  J Clin Immunol       Date:  2013-04-25       Impact factor: 8.317

2.  Juvenile systemic lupus erythematosus and dermatomyositis associated with urticarial vasculitis syndrome: a unique presentation.

Authors:  Patrícia A Macêdo; Carolina B Garcia; Monique K Schmitz; Levi H Jales; Rosa M R Pereira; Jozélio F Carvalho
Journal:  Rheumatol Int       Date:  2010-04-17       Impact factor: 2.631

3.  Hypocomplementemic Urticarial Vasculitis Syndrome in an 8-year-old Boy: A Case Report and Review of Literature.

Authors:  Zakiya Saleh Adnan Al Mosawi; Badriya Ebrahim Ahmed Al Hermi
Journal:  Oman Med J       Date:  2013-07

4.  Hypocomplementemic urticarial vasculitis syndrome in three siblings.

Authors:  Z Birsin Ozçakar; Fatoş Yalçınkaya; F Semsa Altugan; Aslı Kavaz; Arzu Ensari; Mesiha Ekim
Journal:  Rheumatol Int       Date:  2010-11-28       Impact factor: 2.631

Review 5.  Urticarial vasculitis.

Authors:  Joe Venzor; Wai L Lee; David P Huston
Journal:  Clin Rev Allergy Immunol       Date:  2002-10       Impact factor: 8.667

Review 6.  Vasculitis from the pediatric perspective.

Authors:  P A Brogan; M J Dillon
Journal:  Curr Rheumatol Rep       Date:  2000-10       Impact factor: 4.686

7.  A Case of Crescentic Glomerulonephritis Complicated with Hypocomplementemic Urticarial Vasculitis Syndrome and ANCA-Associated Vasculitis.

Authors:  Marenao Tanaka; Norihito Moniwa; Tomohiro Mita; Toshiyuki Tobisawa; Tamaki Matsumoto; Atsushi Mochizuki; Tomohisa Yamashita; Toshiyuki Yano; Masato Furuhashi; Tetsuji Miura
Journal:  Case Rep Nephrol Dial       Date:  2017-11-27
  7 in total

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