Literature DB >> 23904922

Hypocomplementemic Urticarial Vasculitis Syndrome in an 8-year-old Boy: A Case Report and Review of Literature.

Zakiya Saleh Adnan Al Mosawi1, Badriya Ebrahim Ahmed Al Hermi.   

Abstract

Hypocomplementemic urticarial vasculitis syndrome is an immune complex-mediated disease of unknown etiology. The clinical course is characterized by urticaria, conjunctivitis, joint pain, and hypocomplementemia. We here report a case of a child with hypocomplementemic urticarial vasculitis syndrome that progressed to nephritis. Renal biopsy was consistent with diffuse proliferative glomerulonephritis with diffuse subendothelial immune deposits. He responded well to a combination of steroid and mofetil micofenolate.

Entities:  

Keywords:  Children; HUVS; Nephritis

Year:  2013        PMID: 23904922      PMCID: PMC3725255          DOI: 10.5001/omj.2013.76

Source DB:  PubMed          Journal:  Oman Med J        ISSN: 1999-768X


  10 in total

Review 1.  Urticarial vasculitis.

Authors:  R E Berg; G R Kantor; W F Bergfeld
Journal:  Int J Dermatol       Date:  1988-09       Impact factor: 2.736

2.  Hypocomplementemic urticarial vasculitis: report of a pediatric case.

Authors:  M A Cadnapaphornchai; F T Saulsbury; V F Norwood
Journal:  Pediatr Nephrol       Date:  2000-04       Impact factor: 3.714

3.  Hypocomplementemia with cutaneous vasculitis and arthritis. Possible immune complex syndrome.

Authors:  F C McDuffie; W M Sams; J E Maldonado; P H Andreini; D L Conn; E A Samayoa
Journal:  Mayo Clin Proc       Date:  1973-05       Impact factor: 7.616

Review 4.  Urticarial vasculitis: a histopathologic and clinical review of 72 cases.

Authors:  D R Mehregan; M J Hall; L E Gibson
Journal:  J Am Acad Dermatol       Date:  1992-03       Impact factor: 11.527

5.  Rapidly progressive glomerulonephritis in a boy with hypocomplementaemic urticarial vasculitis.

Authors:  M Renard; C Wouters; W Proesmans
Journal:  Eur J Pediatr       Date:  1998-03       Impact factor: 3.183

Review 6.  Hypocomplementemic urticarial vasculitis syndrome: an interdisciplinary challenge.

Authors:  Wolfgang Grotz; Hideo A Baba; Jan U Becker; Martin W Baumgärtel
Journal:  Dtsch Arztebl Int       Date:  2009-11-13       Impact factor: 5.594

7.  Hypocomplementemic urticarial vasculitis syndrome with severe systemic manifestations.

Authors:  A Martini; A Ravelli; S Albani; F De Benedetti; M Massa; J J Wisnieski
Journal:  J Pediatr       Date:  1994-05       Impact factor: 4.406

8.  IgG autoantibody to the collagen-like region of Clq in hypocomplementemic urticarial vasculitis syndrome, systemic lupus erythematosus, and 6 other musculoskeletal or rheumatic diseases.

Authors:  J J Wisnieski; S M Jones
Journal:  J Rheumatol       Date:  1992-06       Impact factor: 4.666

9.  Intravenous immunoglobulin therapy for hypocomplementemic urticarial vasculitis associated with systemic lupus erythematosus in a child.

Authors:  Marco A Yamazaki-Nakashimada; Carola Duran-McKinster; Nadia Ramírez-Vargas; Victor Hernandez-Bautista
Journal:  Pediatr Dermatol       Date:  2009 Jul-Aug       Impact factor: 1.588

10.  Hypocomplementemic urticarial vasculitis: report of a 12-year-old girl with systemic lupus erythematosus.

Authors:  Tracy DeAmicis; Mona Z Mofid; Bernard Cohen; Hossein C Nousari
Journal:  J Am Acad Dermatol       Date:  2002-11       Impact factor: 11.527

  10 in total
  2 in total

Review 1.  Mucocutaneous manifestations in juvenile-onset systemic lupus erythematosus: a review of literature.

Authors:  Direkrit Chiewchengchol; Ruth Murphy; Steven W Edwards; Michael W Beresford
Journal:  Pediatr Rheumatol Online J       Date:  2015-01-05       Impact factor: 3.054

2.  Biopsy-proven kidney involvement in hypocomplementemic urticarial vasculitis.

Authors:  Alice Corthier; Marie Jachiet; Daniel Bertin; Aude Servais; Christelle Barbet; Adrien Bigot; Marie-Sylvie Doutre; Didier Bessis; Ancuta Bouffandeau; Olivier Moranne; Pierre-André Jarrot; Nathalie Bardin; Benjamin Terrier; Stephane Burtey; Xavier Puéchal; Laurent Daniel; Noémie Jourde-Chiche
Journal:  BMC Nephrol       Date:  2022-02-16       Impact factor: 2.388

  2 in total

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