Literature DB >> 7837769

Urinary propionylcarnitine analysis for monitoring carnitine supplementation in inherited disorders of propionate metabolism.

N Sugiyama1, I Matsuda, Y Wada, K Narisawa, M Kobayashi, K Kidouchi.   

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Year:  1994        PMID: 7837769     DOI: 10.1007/bf00711600

Source DB:  PubMed          Journal:  J Inherit Metab Dis        ISSN: 0141-8955            Impact factor:   4.982


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  5 in total

1.  An improved and simplified radioisotopic assay for the determination of free and esterified carnitine.

Authors:  J D McGarry; D W Foster
Journal:  J Lipid Res       Date:  1976-05       Impact factor: 5.922

2.  Analytical method for urinary glutarylcarnitine, acetylcarnitine and propionylcarnitine with a carboxylic acid analyser and a reversed-phase column.

Authors:  K Kidouchi; N Sugiyama; H Morishita; Y Wada; S Nagai; J Sakakibara
Journal:  J Chromatogr       Date:  1987-12-25

3.  Biochemical evidence of carnitine effect on propionate elimination.

Authors:  N Sugiyama; H Morishita; S Nagaya; T Nakajima; A Kawase; A Ohya; S Sugiyama; K Kamiya; I Watanabe; H Togari
Journal:  J Inherit Metab Dis       Date:  1984       Impact factor: 4.982

4.  L-carnitine enhances excretion of propionyl coenzyme A as propionylcarnitine in propionic acidemia.

Authors:  C R Roe; D S Millington; D A Maltby; T P Bohan; C L Hoppel
Journal:  J Clin Invest       Date:  1984-06       Impact factor: 14.808

5.  Carnitine deficiency in inherited organic acid disorders and Reye syndrome.

Authors:  N Sugiyama; K Kidouchi; M Kobayashi; Y Wada
Journal:  Acta Paediatr Jpn       Date:  1990-08
  5 in total

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