Literature DB >> 6859223

The twitcher mouse. A model of human globoid cell leukodystrophy (krabbe's disease).

K Suzuki, K Suzuki.   

Abstract

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Year:  1983        PMID： 6859223      PMCID： PMC1916270     

Source DB:  PubMed          Journal:  Am J Pathol        ISSN： 0002-9440            Impact factor:   4.307


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  12 in total

1.  Globoid cell leukodystrophy: deficiency of lactosyl ceramide beta-galactosidase.

Authors:  D A Wenger; M Sattler; W Hiatt
Journal:  Proc Natl Acad Sci U S A       Date:  1974-03       Impact factor: 11.205

2.  The twitcher mouse: determination of genetic status by galactosylceramidase assays on clipped tail.

Authors:  T Kobayashi; H Nagara; K Suzuki; K Suzuki
Journal:  Biochem Med       Date:  1982-02

3.  Animal model: globoid cell leukodystrophy in the dog.

Authors:  T F Fletcher; H J Kurtz
Journal:  Am J Pathol       Date:  1972-02       Impact factor: 4.307

4.  Lactosylceramide beta-galactosidase in human sphingolipidoses. Evidence for two genetically distinct enzymes.

Authors:  H Tanaka; K Suzuki
Journal:  J Biol Chem       Date:  1975-03-25       Impact factor: 5.157

5.  Improved myelination in nerve grafts from the leucodystrophic twitcher into trembler mice: evidence for enzyme replacement.

Authors:  F Scaravilli; J M Jacobs
Journal:  Brain Res       Date:  1982-04-08       Impact factor: 3.252

6.  The Twitcher mouse: an enzymatically authentic model of human globoid cell leukodystrophy (Krabbe disease).

Authors:  T Kobayashi; T Yamanaka; J M Jacobs; F Teixeira; K Suzuki
Journal:  Brain Res       Date:  1980-12-08       Impact factor: 3.252

7.  Globoid cell leucodystrophy (Krabbe's disease): deficiency of galactocerebroside beta-galactosidase.

Authors:  K Suzuki; Y Suzuki
Journal:  Proc Natl Acad Sci U S A       Date:  1970-06       Impact factor: 11.205

8.  Globoid cell leucodystrophy in polled Dorset sheep.

Authors:  D H Pritchard; D V Napthine; A J Sinclair
Journal:  Vet Pathol       Date:  1980-07       Impact factor: 2.221

9.  Hereditary leucodystrophy in the mouse: the new mutant twitcher.

Authors:  L W Duchen; E M Eicher; J M Jacobs; F Scaravilli; F Teixeira
Journal:  Brain       Date:  1980-09       Impact factor: 13.501

10.  Peripheral nerve grafts in hereditary leukodystrophic mutant mice (twitcher).

Authors:  F Scaravilli; J M Jacobs
Journal:  Nature       Date:  1981-03-05       Impact factor: 49.962
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  22 in total

1.  Factors that affect postnatal bone growth retardation in the twitcher murine model of Krabbe disease.

Authors:  Miguel Agustin Contreras; William Louis Ries; Srinivasan Shanmugarajan; Gonzalo Arboleda; Inderjit Singh; Avtar Kaur Singh
Journal:  Biochim Biophys Acta       Date:  2010-05-02

2.  Effects of irradiation on the postnatal development of the brain in a genetic mouse model of globoid cell leukodystrophy.

Authors:  Francesca Galbiati; Giulia Clementi; Daniela Superchi; Maria I Givogri; Ernesto R Bongarzone
Journal:  Neurochem Res       Date:  2007-01-03       Impact factor: 3.996

3.  Mechanism-based combination treatment dramatically increases therapeutic efficacy in murine globoid cell leukodystrophy.

Authors:  Jacqueline A Hawkins-Salsbury; Lauren Shea; Xuntian Jiang; Daniel A Hunter; A Miguel Guzman; Adarsh S Reddy; Elizabeth Y Qin; Yedda Li; Steven J Gray; Daniel S Ory; Mark S Sands
Journal:  J Neurosci       Date:  2015-04-22       Impact factor: 6.167

Review 4.  Cellular transplant therapies for globoid cell leukodystrophy: Preclinical and clinical observations.

Authors:  Keri R Maher; Andrew M Yeager
Journal:  J Neurosci Res       Date:  2016-11       Impact factor: 4.164

Review 5.  Treatment for Krabbe's disease: Finding the combination.

Authors:  Christina R Mikulka; Mark S Sands
Journal:  J Neurosci Res       Date:  2016-11       Impact factor: 4.164

Review 6.  Lysosomal enzyme replacement therapies: Historical development, clinical outcomes, and future perspectives.

Authors:  Melani Solomon; Silvia Muro
Journal:  Adv Drug Deliv Rev       Date:  2017-05-11       Impact factor: 15.470

7.  The structural and functional role of myelin fast-migrating cerebrosides: pathological importance in multiple sclerosis.

Authors:  Maria Podbielska; Steven B Levery; Edward L Hogan
Journal:  Clin Lipidol       Date:  2011-04

8.  Cell-autonomous expression of the acid hydrolase galactocerebrosidase.

Authors:  Christina R Mikulka; Joshua T Dearborn; Bruno A Benitez; Amy Strickland; Lin Liu; Jeffrey Milbrandt; Mark S Sands
Journal:  Proc Natl Acad Sci U S A       Date:  2020-04-06       Impact factor: 11.205

Review 9.  Peroxisomal dysfunction in inflammatory childhood white matter disorders: an unexpected contributor to neuropathology.

Authors:  Inderjit Singh; Avtar K Singh; Miguel A Contreras
Journal:  J Child Neurol       Date:  2009-07-15       Impact factor: 1.987

10.  Clinical and immunopathologic alterations in rhesus macaques affected with globoid cell leukodystrophy.

Authors:  Juan T Borda; Xavier Alvarez; Mahesh Mohan; Marion S Ratterree; Kathrine Phillippi-Falkenstein; Andrew A Lackner; Bruce A Bunnell
Journal:  Am J Pathol       Date:  2007-12-28       Impact factor: 4.307
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