Literature DB >> 6476881

Familial persistent pulmonary hypertension.

I Shohet, B Reichman, G Schibi, M Brish.   

Abstract

We report three siblings who presented with a clinical picture of persistent pulmonary hypertension of newborn and died between 4 and 15 days of age. Pulmonary artery pressure in all was above systemic values, with a right to left shunt via either the foramen ovale or ductus arteriosus, or both. Histology of the pulmonary vascular bed showed extension of muscle into small arteries which are normally non-muscular.

Entities:  

Mesh：

Year:  1984        PMID： 6476881      PMCID： PMC1628623          DOI： 10.1136/adc.59.8.783

Source DB:  PubMed          Journal:  Arch Dis Child        ISSN： 0003-9888            Impact factor:   3.791


  4 in total

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Authors:  S J Goldberg; R A Levy; B Siassi; J Betten
Journal:  Pediatrics       Date:  1971-10       Impact factor: 7.124

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Authors:  W H Drummond; G J Peckham; W W Fox
Journal:  Clin Pediatr (Phila)       Date:  1977-04       Impact factor: 1.168

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Authors:  S G Haworth; L Reid
Journal:  J Pediatr       Date:  1976-04       Impact factor: 4.406

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Authors:  D L Levin; D E Fixler; F C Morriss; J Tyson
Journal:  J Pediatr       Date:  1978-03       Impact factor: 4.406
  4 in total
  4 in total

1.  Familial persistent pulmonary hypertension of the newborn resulting from misalignment of the pulmonary vessels (congenital alveolar capillary dysplasia).

Authors:  H B Vassal; M Malone; A J Petros; R M Winter
Journal:  J Med Genet       Date:  1998-01       Impact factor: 6.318

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Authors:  I D Young; A B Rickett; M Clarke
Journal:  J Med Genet       Date:  1986-02       Impact factor: 6.318

3.  A familial case of alveolar capillary dysplasia with misalignment of pulmonary veins supports paternal imprinting of FOXF1 in human.

Authors:  Partha Sen; Romana Gerychova; Petr Janku; Marta Jezova; Iveta Valaskova; Colby Navarro; Iris Silva; Claire Langston; Stephen Welty; John Belmont; Pawel Stankiewicz
Journal:  Eur J Hum Genet       Date:  2012-09-19       Impact factor: 4.246

4.  Comparative analyses of lung transcriptomes in patients with alveolar capillary dysplasia with misalignment of pulmonary veins and in foxf1 heterozygous knockout mice.

Authors:  Partha Sen; Avinash V Dharmadhikari; Tadeusz Majewski; Mahmoud A Mohammad; Tanya V Kalin; Joanna Zabielska; Xiaomeng Ren; Molly Bray; Hannah M Brown; Stephen Welty; Sundararajah Thevananther; Claire Langston; Przemyslaw Szafranski; Monica J Justice; Vladimir V Kalinichenko; Anna Gambin; John Belmont; Pawel Stankiewicz
Journal:  PLoS One       Date:  2014-04-10       Impact factor: 3.240
  4 in total

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