Literature DB >> 6331159

Metastatic islet cell tumor in von Hippel-Lindau disease.

D Cornish, A Pont, D Minor, J L Coombs, J Bennington.   

Abstract

A 56-year-old woman with many unusual manifestations of von Hippel-Lindau syndrome is described. In addition to retinal hemangioblastomas, pheochromocytoma, renal cell carcinoma, and multiple organ cysts, she had a cerebellar astrocytoma, pancreatic exocrine insufficiency, diabetes mellitus, thyrotoxicosis, and a metastatic calcitonin-secreting islet cell carcinoma. This case report documents the first example of a metastatic islet cell tumor in a patient with von Hippel-Lindau disease. The possible relationship between this disorder, the other neurocutaneous syndromes, and the multiple endocrine neoplasia syndromes is discussed.

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Year:  1984        PMID： 6331159     DOI： 10.1016/0002-9343(84)90450-9

Source DB:  PubMed          Journal:  Am J Med        ISSN： 0002-9343            Impact factor:   4.965


  9 in total

1.  Surgical decision-making affected by clinical and genetic screening of a novel kindred with von Hippel-Lindau disease and pancreatic islet cell tumors.

Authors:  S A Curley; S T Lott; J W Luca; M L Frazier; A M Killary
Journal:  Ann Surg       Date:  1998-02       Impact factor: 12.969

2.  Pancreatic cystic manifestations in von Hippel-Lindau disease.

Authors:  R Girelli; C Bassi; M Falconi; L De Santis; A Bonora; E Caldiron; N Sartori; R Salvia; G Briani; P Pederzoli
Journal:  Int J Pancreatol       Date:  1997-10

Review 3.  Calcitonin-Producing Neuroendocrine Neoplasms of the Pancreas: Clinicopathological Study of 25 Cases and Review of the Literature.

Authors:  Silvia Uccella; Annika Blank; Roberta Maragliano; Fausto Sessa; Aurel Perren; Stefano La Rosa
Journal:  Endocr Pathol       Date:  2017-12       Impact factor: 3.943

4.  Von Hippel-Lindau disease complicated by acute pancreatitis and Evan's syndrome.

Authors:  S Tenner; A Roston; D Lichtenstein; G Sica; D Carr-Locke; P A Banks
Journal:  Int J Pancreatol       Date:  1995-12

5.  Malignant glioma arising at the site of an excised cerebellar hemangioblastoma after irradiation in a von Hippel-Lindau disease patient.

Authors:  Na-Hye Myong; Bong-Jin Park
Journal:  Yonsei Med J       Date:  2009-08-19       Impact factor: 2.759

6.  Central nervous system lesions in von Hippel-Lindau syndrome.

Authors:  H P Neumann; H R Eggert; R Scheremet; M Schumacher; M Mohadjer; A K Wakhloo; B Volk; U Hettmannsperger; P Riegler; P Schollmeyer
Journal:  J Neurol Neurosurg Psychiatry       Date:  1992-10       Impact factor: 10.154

7.  Esophagogastric varices due to arterioportal shunt in a serous cystadenoma of the pancreas in von Hippel-Lindau disease.

Authors:  Masatsugu Okuyama; Yasuhiro Fujiwara; Tsuyoshi Hayakawa; Masatsugu Shiba; Toshio Watanabe; Kazunari Tominaga; Akihiro Tamori; Nobuhide Oshitani; Kazuhide Higuchi; Takayuki Matsumoto; Kenji Nakamura; Kenichi Wakasa; Kazuhiro Hirohashi; Shingo Ashida; Taro Shuin; Tetsuo Arakawa
Journal:  Dig Dis Sci       Date:  2003-10       Impact factor: 3.199

8.  Multiple neuroendocrine tumors of the pancreas in von Hippel-Lindau disease patients: histopathological and molecular genetic analysis.

Authors:  I A Lubensky; S Pack; D Ault; A O Vortmeyer; S K Libutti; P L Choyke; M M Walther; W M Linehan; Z Zhuang
Journal:  Am J Pathol       Date:  1998-07       Impact factor: 4.307

9.  Von Hippel-Lindau disease presenting as pancreatic neuroendocrine tumour.

Authors:  S L Mount; D L Weaver; D J Taatjes; W C McKinnon; J C Hebert
Journal:  Virchows Arch       Date:  1995       Impact factor: 4.064
  9 in total

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