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Abstract
Mesh: See more » AnimalsCarbohydrate Metabolism, Inborn Errors/enzymologyDiffuse Cerebral Sclerosis of Schilder/enzymologyDiffuse Cerebral Sclerosis of Schilder/geneticsFucoseGalactosamineGalactosidases/metabolismGangliosides/metabolismGaucher Disease/enzymologyGlucosidases/metabolismGlucuronidase/analysisGlucuronidase/metabolismGlycoside Hydrolases/metabolismGolgi Apparatus/enzymologyHexosaminidases/metabolismHumansHydrogen-Ion ConcentrationIsoenzymes/metabolismLeukodystrophy, Metachromatic/enzymologyLipidoses/enzymologyLysosomes/enzymologyMannoseNeuraminidase/metabolismSerineXylose
Substances: See more » GangliosidesIsoenzymesFucoseSerineGalactosamineXyloseGalactosidasesGlucosidasesGlycoside HydrolasesHexosaminidasesNeuraminidaseGlucuronidaseMannose
Year: 1973 PMID: 4594433 DOI: 10.1007/bf01795471
Source DB: PubMed Journal: Mol Cell Biochem ISSN: 0300-8177 Impact factor: 3.396