Literature DB >> 4182334

Cirrhosis associated with alpha-1-antitrypsin deficiency: a previously unrecognized inherited disorder.

H L Sharp, R A Bridges, W Krivit, E F Freier.   

Abstract

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Year:  1969        PMID: 4182334

Source DB:  PubMed          Journal:  J Lab Clin Med        ISSN: 0022-2143


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  149 in total

1.  Proteinase inhibitors in rheumatoid arthritis.

Authors:  D Brackertz; J Hagmann; F Kueppers
Journal:  Ann Rheum Dis       Date:  1975-06       Impact factor: 19.103

2.  Polymorphism of alpha1-antitrypsin in a Portuguese population.

Authors:  H M Geada; J A Albino; C Manso
Journal:  Hum Genet       Date:  1976-05-19       Impact factor: 4.132

3.  Molecular abnormality of human alpha1-antitrypsin variant (Pi-ZZ) associated with plasma activity deficiency.

Authors:  A Yoshida; J Lieberman; L Gaidulis; C Ewing
Journal:  Proc Natl Acad Sci U S A       Date:  1976-04       Impact factor: 11.205

4.  Does alpha-1-antitrypsin P1 null phenotype exist?

Authors:  J P Martin; R Sesboue; R Charlionet; C Ropartz
Journal:  Humangenetik       Date:  1975-11-06

5.  Alpha(1)-Antitrypsin Deficiency.

Authors: 
Journal:  Curr Treat Options Gastroenterol       Date:  2000-12

6.  The mechanism of fibril formation of a non-inhibitory serpin ovalbumin revealed by the identification of amyloidogenic core regions.

Authors:  Naoki Tanaka; Yumi Morimoto; Yurika Noguchi; Tomoko Tada; Tomonori Waku; Shigeru Kunugi; Takashi Morii; Yin-Fai Lee; Takashi Konno; Nobuyuki Takahashi
Journal:  J Biol Chem       Date:  2010-12-14       Impact factor: 5.157

7.  The effect of neuraminidase on genetic variants of alpha anitrypsin.

Authors:  D W Cox
Journal:  Am J Hum Genet       Date:  1975-03       Impact factor: 11.025

Review 8.  Gene therapy for alpha-1 antitrypsin deficiency.

Authors:  Terence R Flotte; Christian Mueller
Journal:  Hum Mol Genet       Date:  2011-04-16       Impact factor: 6.150

9.  Multiple tissues express alpha 1-antitrypsin in transgenic mice and man.

Authors:  J A Carlson; B B Rogers; R N Sifers; H K Hawkins; M J Finegold; S L Woo
Journal:  J Clin Invest       Date:  1988-07       Impact factor: 14.808

10.  Liver replacement for alpha1-antitrypsin deficiency.

Authors:  C W Putnam; K A Porter; R L Peters; M Ashcavai; A G Redeker; T E Starzl
Journal:  Surgery       Date:  1977-03       Impact factor: 3.982

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