| Literature DB >> 35005626 |
Akshata Pandit1, Lai Wei2, Luis Bustamante1, Patrick Elder3, William B S Falk3, Megan Sell3, Ashley Rosko3, Don M Benson3, Steven M Devine3, Craig C Hofmeister3, Yvonne A Efebera3.
Abstract
To date, there is no standard of care for patients with newly diagnosed Primary (AL) amyloidosis. Autologous hematopoietic stem cell transplant (aHSCT) is a reasonable option, but has been limited in its use due to increase in treatment-related mortality (TRM). We retrospectively analyzed the outcomes of 42 newly diagnosed consecutive AL amyloidosis patients transplanted at our center. The median age at aHSCT was 57.5 (range 26-71). Twenty one (50%) had involvement of at least two organs and 40 (97%) patients had cardiac stage I or II. Patients received high dose Melphalan 140(n=4) or 200(n=38) mg/m2. Median times to neutrophil and platelet engraftments were 12 and 18 days, respectively. Three months hematologic response were complete response in 21 patients (50%), very good partial response in 4 (10%), partial response in 5 (12%) and Minimal/Stable disease in 6(15%). The respective 1, 3, and 5 year progression-free survival were 79%, 67% and 57%, and overall survival from Transplant 81%, 73% and 66%. Day 100 and 1 year TRM were 4.8% and 7.1% respectively. Our results show that aHSCT is a safe and reasonable option for patients with AL amyloidosis. Day 100 and 1 year TRM compares favorably to multiple myeloma patients undergoing aHSCT.Entities:
Keywords: AL amyloid; Light chain Amyloidosis; Primary Amyloidosis; Transplantation; amyloidosis
Year: 2019 PMID: 35005626 PMCID: PMC8734359
Source DB: PubMed Journal: Arch Hematol Blood Dis ISSN: 2639-3581