Literature DB >> 34350858

Safety and Effectiveness of Recombinant Human Growth Hormone in Children with Turner Syndrome: Data from the PATRO Children Study.

Philippe Backeljauw1, Shankar Kanumakala2, Sandro Loche3, Karl Otfried Schwab4, Roland Werner Pfäffle5, Charlotte Höybye6,7, Elena Lundberg8, Tadej Battelino9, Berit Kriström8, Tomasz Giemza10, Hichem Zouater11.   

Abstract

INTRODUCTION: PATRO Children is an international, observational, postmarketing surveillance study for a biosimilar recombinant human growth hormone (rhGH; somatropin, Omnitrope®; Sandoz), approved by the European Medicines Agency in 2006. We report safety and effectiveness data for patients with Turner syndrome (TS).
METHODS: The study population included infants, children, and adolescents with TS who received Omnitrope® treatment according to standard clinical practice. Adverse events (AEs) were monitored for safety evaluation, and height velocity (HV), height standard deviation score (HSDS), and HVSDS were calculated to evaluate treatment effectiveness.
RESULTS: As of August 2019, 348 TS patients were enrolled from 130 centers. At baseline, 314 patients (90.2%) were prepubertal and 284 patients (81.6%) were rhGH treatment naïve. The mean (range) age at baseline was 9.0 (0.7-18.5) years, and mean (SD) treatment duration in the study was 38.5 (26.8) months. Overall, 170 patients (48.9%) reported AEs, which were considered treatment related in 25 patients (7.2%). One treatment-related serious AE was reported (intracranial hypertension). Mean ΔHSDS after 3 years of therapy was +1.17 in treatment-naïve prepubertal patients and +0.1 in pretreated prepubertal patients. In total, 51 patients (31.1%) reached adult height (AH), 35 of whom were rhGH treatment naïve; in these patients, mean (SD) HSDS was -2.97 (1.03) at the start of Omnitrope® treatment, and they achieved a mean (SD) AHSDS of -2.02 (0.9).
CONCLUSION: These data suggest that biosimilar rhGH is well tolerated and effective in TS patients managed in real-life clinical practice. Optimization of rhGH dose may contribute to a higher AH. The Author(s). Published by S. Karger AG, Basel.

Entities:  

Keywords:  Growth hormone replacement therapy; PATRO Children; Pediatric endocrinology; Turner syndrome

Mesh:

Substances:

Year:  2021        PMID: 34350858      PMCID: PMC8491505          DOI: 10.1159/000515875

Source DB:  PubMed          Journal:  Horm Res Paediatr        ISSN: 1663-2818            Impact factor:   2.852


  30 in total

1.  Prediction of long-term response to recombinant human growth hormone in Turner syndrome: development and validation of mathematical models. KIGS International Board. Kabi International Growth Study.

Authors:  M B Ranke; A Lindberg; P Chatelain; P Wilton; W Cutfield; K Albertsson-Wikland; D A Price
Journal:  J Clin Endocrinol Metab       Date:  2000-11       Impact factor: 5.958

2.  The calculation of target height reconsidered.

Authors:  M Hermanussen; J Cole
Journal:  Horm Res       Date:  2003

3.  Response to three years of growth hormone therapy in girls with Turner syndrome.

Authors:  Hong Kyu Park; Hae Sang Lee; Jung Hee Ko; Il Tae Hwang; Jin Soon Hwang
Journal:  Ann Pediatr Endocrinol Metab       Date:  2013-03-31

4.  Standards for children's height at ages 2-9 years allowing for heights of parents.

Authors:  J M Tanner; H Goldstein; R H Whitehouse
Journal:  Arch Dis Child       Date:  1970-12       Impact factor: 3.791

5.  Prospective study confirms oxandrolone-associated improvement in height in growth hormone-treated adolescent girls with Turner syndrome.

Authors:  Martha P D Zeger; Kavita Shah; Karen Kowal; Gordon B Cutler; Harvey Kushner; Judith L Ross
Journal:  Horm Res Paediatr       Date:  2010-08-20       Impact factor: 2.852

Review 6.  Turner syndrome: mechanisms and management.

Authors:  Claus H Gravholt; Mette H Viuff; Sara Brun; Kirstine Stochholm; Niels H Andersen
Journal:  Nat Rev Endocrinol       Date:  2019-06-18       Impact factor: 43.330

7.  Long-term safety of recombinant human growth hormone in children.

Authors:  J Bell; K L Parker; R D Swinford; A R Hoffman; T Maneatis; B Lippe
Journal:  J Clin Endocrinol Metab       Date:  2009-11-11       Impact factor: 5.958

8.  Growth hormone treatment of Canadian children: results from the GeNeSIS phase IV prospective observational study.

Authors:  Cheri Deal; Susan Kirsch; Jean-Pierre Chanoine; Sarah Lawrence; Elizabeth Cummings; Elizabeth T Rosolowsky; Seth D Marks; Nan Jia; Christopher J Child
Journal:  CMAJ Open       Date:  2018-09-10

9.  Harmonizing national growth references for multi-centre surveys, drug monitoring and international postmarketing surveillance.

Authors:  M Hermanussen; C Assmann; H Wöhling; M Zabransky
Journal:  Acta Paediatr       Date:  2011-08-11       Impact factor: 2.299

10.  Mode of clinical presentation and delayed diagnosis of Turner syndrome: a single Centre UK study.

Authors:  Louise Apperley; Urmi Das; Renuka Ramakrishnan; Poonam Dharmaraj; Jo Blair; Mohammed Didi; Senthil Senniappan
Journal:  Int J Pediatr Endocrinol       Date:  2018-06-26
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