Literature DB >> 24904845

Response to three years of growth hormone therapy in girls with Turner syndrome.

Hong Kyu Park1, Hae Sang Lee2, Jung Hee Ko2, Il Tae Hwang1, Jin Soon Hwang2.   

Abstract

PURPOSE: Short stature is the most common finding in patients with Turner syndrome. Improving the final adult height in these patients is a challenge both for the patients and physicians. We investigated the clinical response of patients to growth hormone treatment for height improvement over the period of three years.
METHODS: Review of medical records from 27 patients with Turner syndrome treated with recombinant human growth hormone for more than 3 years was done. Differences in the changes of height standard deviation scores according to karyotype were measured and factors influencing the height changes were analyzed.
RESULTS: The response to recombinant human growth hormone was an increase in the height of the subjects to a mean value of 1.1 standard deviation for subjects with Turner syndrome at the end of the 3-year treatment. The height increment in the first year was highest. The height standard deviation score in the third year was negatively correlated with the age at the beginning of the recombinant human growth hormone treatment. Different karyotypes in subjects did not seem to affect the height changes.
CONCLUSION: Early growth hormone administration in subjects with Turner syndrome is helpful to improve height response to the treatment.

Entities:  

Keywords:  Growth hormone; Treatment outcome; Turner syndrome

Year:  2013        PMID: 24904845      PMCID: PMC4027066          DOI: 10.6065/apem.2013.18.1.13

Source DB:  PubMed          Journal:  Ann Pediatr Endocrinol Metab        ISSN: 2287-1012


  36 in total

1.  Transcriptional and translational regulation of the Leri-Weill and Turner syndrome homeobox gene SHOX.

Authors:  Rudiger J Blaschke; Christine Töpfer; Antonio Marchini; Herbert Steinbeisser; Johannes W G Janssen; Gudrun A Rappold
Journal:  J Biol Chem       Date:  2003-09-05       Impact factor: 5.157

2.  Growth hormone therapy of Turner syndrome: the impact of age of estrogen replacement on final height. Genentech, Inc., Collaborative Study Group.

Authors:  S D Chernausek; K M Attie; J F Cara; R G Rosenfeld; J Frane
Journal:  J Clin Endocrinol Metab       Date:  2000-07       Impact factor: 5.958

3.  Pseudoautosomal deletions encompassing a novel homeobox gene cause growth failure in idiopathic short stature and Turner syndrome.

Authors:  E Rao; B Weiss; M Fukami; A Rump; B Niesler; A Mertz; K Muroya; G Binder; S Kirsch; M Winkelmann; G Nordsiek; U Heinrich; M H Breuning; M B Ranke; A Rosenthal; T Ogata; G A Rappold
Journal:  Nat Genet       Date:  1997-05       Impact factor: 38.330

4.  Variable effect of growth hormone on growth and final adult height in Scottish patients with Turner's syndrome.

Authors:  C E Chu; W F Paterson; C J Kelnar; P J Smail; S A Greene; M D Donaldson
Journal:  Acta Paediatr       Date:  1997-02       Impact factor: 2.299

5.  Growth hormone and low dose estrogen in Turner syndrome: results of a United States multi-center trial to near-final height.

Authors:  Charmian A Quigley; Brenda J Crowe; D Greg Anglin; John J Chipman
Journal:  J Clin Endocrinol Metab       Date:  2002-05       Impact factor: 5.958

6.  Early treatment with GH alone in Turner syndrome: prepubertal catch-up growth and waning effect.

Authors:  Malgorzata Wasniewska; Filippo De Luca; Rosalba Bergamaschi; Maria Pia Guarneri; Laura Mazzanti; Patrizia Matarazzo; Antonella Petri; Giuseppe Crisafulli; Giuseppina Salzano; Fortunato Lombardo
Journal:  Eur J Endocrinol       Date:  2004-11       Impact factor: 6.664

7.  Turner syndrome and Xp deletions: clinical and molecular studies in 47 patients.

Authors:  T Ogata; K Muroya; N Matsuo; O Shinohara; T Yorifuji; Y Nishi; Y Hasegawa; R Horikawa; K Tachibana
Journal:  J Clin Endocrinol Metab       Date:  2001-11       Impact factor: 5.958

8.  Impact of growth hormone therapy on quality of life in adults with turner syndrome.

Authors:  Emily Amundson; Ulla Wide Boman; Marie-Louise Barrenäs; Inger Bryman; Kerstin Landin-Wilhelmsen
Journal:  J Clin Endocrinol Metab       Date:  2010-01-15       Impact factor: 5.958

9.  Growth failure in early life: an important manifestation of Turner syndrome.

Authors:  Michael L Davenport; Natavut Punyasavatsut; Paul W Stewart; Daniel F Gunther; Lars Sävendahl; Virginia P Sybert
Journal:  Horm Res       Date:  2002

10.  Decreased growth hormone response to growth hormone-releasing hormone in Turner's syndrome: relation to body weight and adiposity.

Authors:  J C Reiter; M Craen; G Van Vliet
Journal:  Acta Endocrinol (Copenh)       Date:  1991-07
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  4 in total

1.  Safety Outcomes and Near-Adult Height Gain of Growth Hormone-Treated Children with SHOX Deficiency: Data from an Observational Study and a Clinical Trial.

Authors:  Imane Benabbad; Myriam Rosilio; Christopher J Child; Jean-Claude Carel; Judith L Ross; Cheri L Deal; Stenvert L S Drop; Alan G Zimmermann; Nan Jia; Charmian A Quigley; Werner F Blum
Journal:  Horm Res Paediatr       Date:  2016-12-22       Impact factor: 2.852

2.  Turner syndrome with spinal hemorrhage due to vascular malformation.

Authors:  Min Kyung Yu; Mo Kyung Jung; Ki Eun Kim; Ah Reum Kwon; Hyun Wook Chae; Duk Hee Kim; Ho-Seong Kim
Journal:  Ann Pediatr Endocrinol Metab       Date:  2015-12-31

3.  Recombinant growth hormone therapy in children with short stature in Kuwait: a cross-sectional study of use and treatment outcomes.

Authors:  Dalia Al-Abdulrazzaq; Abdullah Al-Taiar; Kholoud Hassan; Iman Al-Basari
Journal:  BMC Endocr Disord       Date:  2015-12-03       Impact factor: 2.763

4.  Safety and Effectiveness of Recombinant Human Growth Hormone in Children with Turner Syndrome: Data from the PATRO Children Study.

Authors:  Philippe Backeljauw; Shankar Kanumakala; Sandro Loche; Karl Otfried Schwab; Roland Werner Pfäffle; Charlotte Höybye; Elena Lundberg; Tadej Battelino; Berit Kriström; Tomasz Giemza; Hichem Zouater
Journal:  Horm Res Paediatr       Date:  2021-07-07       Impact factor: 2.852

  4 in total

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