Literature DB >> 33498176

Differential microRNA Expression in USP8-Mutated and Wild-Type Corticotroph Pituitary Tumors Reflect the Difference in Protein Ubiquitination Processes.

Mateusz Bujko1, Paulina Kober1, Joanna Boresowicz1, Natalia Rusetska1, Natalia Zeber-Lubecka2, Agnieszka Paziewska3, Monika Pekul4, Grzegorz Zielinski5, Andrzej Styk5, Jacek Kunicki6, Jerzy Ostrowski2,7, Janusz A Siedlecki1, Maria Maksymowicz4.   

Abstract

USP8 mutations are the most common driver changes in corticotroph pituitary tumors. They have direct effect on cells' proteome through disturbance of ubiquitination process and also influence gene expression. The aim of this study was to compare microRNA profiles in USP8-mutated and wild-type tumors and determine the probable role of differential microRNA expression by integrative microRNA and mRNA analysis.
METHODS: Patients with Cushing's disease (n = 28) and silent corticotroph tumors (n = 20) were included. USP8 mutations were identified with Sanger sequencing. MicroRNA and gene expression was determined with next-generation sequencing. USP8-mutated patients with Cushing's disease showed higher rate of clinical remission and trend towards lower tumor volume than wild-type patients. Comparison of microRNA profiles of USP8-mutated and wild-type tumors revealed 68 differentially expressed microRNAs. Their target genes were determined by in silico prediction and microRNA/mRNA correlation analysis. GeneSet Enrichment analysis of putative targets showed that the most significantly overrepresented genes are involved in protein ubiquitination-related processes. Only few microRNAs influence the expression of genes differentially expressed between USP8-mutated and wild-type tumors.
CONCLUSIONS: Differences in microRNA expression in corticotropinomas stratified according to USP8 status reflect disturbed ubiquitination processes, but do not correspond to differences in gene expression between these tumors.

Entities:  

Keywords:  Cushing’s disease; USP48; USP8; corticotroph PitNET; gene expression; miRNA expression; mutation; next generation sequencing

Year:  2021        PMID: 33498176      PMCID: PMC7863919          DOI: 10.3390/jcm10030375

Source DB:  PubMed          Journal:  J Clin Med        ISSN: 2077-0383            Impact factor:   4.241


  38 in total

1.  The USP8 mutational status may predict long-term remission in patients with Cushing's disease.

Authors:  Adriana Albani; Luis G Pérez-Rivas; Christina Dimopoulou; Stephanie Zopp; Paula Colón-Bolea; Sigrun Roeber; Jürgen Honegger; Jörg Flitsch; Walter Rachinger; Michael Buchfelder; Günter K Stalla; Jochen Herms; Martin Reincke; Marily Theodoropoulou
Journal:  Clin Endocrinol (Oxf)       Date:  2018-06-29       Impact factor: 3.478

Review 2.  MicroRNAs in cancer: biomarkers, functions and therapy.

Authors:  Josie Hayes; Pier Paolo Peruzzi; Sean Lawler
Journal:  Trends Mol Med       Date:  2014-07-12       Impact factor: 11.951

3.  MicroRNA 375 mediates the signaling pathway of corticotropin-releasing factor (CRF) regulating pro-opiomelanocortin (POMC) expression by targeting mitogen-activated protein kinase 8.

Authors:  Nan Zhang; Jun-kai Lin; Juan Chen; Xiong-fei Liu; Jia-li Liu; Hao-shu Luo; Yue-qin Li; Sheng Cui
Journal:  J Biol Chem       Date:  2013-02-21       Impact factor: 5.157

4.  Cushing's disease due to somatic USP8 mutations: a systematic review and meta-analysis.

Authors:  Ingrid Quevedo Wanichi; Beatriz Marinho de Paula Mariani; Fernando Pereira Frassetto; Sheila Aparecida Coelho Siqueira; Nina Rosa de Castro Musolino; Malebranche Berardo Carneiro Cunha-Neto; Gilberto Ochman; Valter Angelo Sperling Cescato; Marcio Carlos Machado; Ericka Barbosa Trarbach; Marcello Delano Bronstein; Maria Candida Barisson Villares Fragoso
Journal:  Pituitary       Date:  2019-08       Impact factor: 4.107

5.  Gas1 Inhibits Metastatic and Metabolic Phenotypes in Colorectal Carcinoma.

Authors:  Qingguo Li; Yi Qin; Ping Wei; Peng Lian; Yaqi Li; Ye Xu; Xinxiang Li; Dawei Li; Sanjun Cai
Journal:  Mol Cancer Res       Date:  2016-07-11       Impact factor: 5.852

6.  Clinical characteristics and surgical outcome in USP8-mutated human adrenocorticotropic hormone-secreting pituitary adenomas.

Authors:  Marco Losa; Pietro Mortini; Angela Pagnano; Mario Detomas; Maria Francesca Cassarino; Francesca Pecori Giraldi
Journal:  Endocrine       Date:  2018-10-12       Impact factor: 3.633

7.  Biophysical and structural insight into the USP8/14-3-3 interaction.

Authors:  Federica Centorrino; Alice Ballone; Madita Wolter; Christian Ottmann
Journal:  FEBS Lett       Date:  2018-03-02       Impact factor: 4.124

8.  Recurrent gain-of-function USP8 mutations in Cushing's disease.

Authors:  Zeng-Yi Ma; Zhi-Jian Song; Jian-Hua Chen; Yong-Fei Wang; Shi-Qi Li; Liang-Fu Zhou; Ying Mao; Yi-Ming Li; Rong-Gui Hu; Zhao-Yun Zhang; Hong-Ying Ye; Ming Shen; Xue-Fei Shou; Zhi-Qiang Li; Hong Peng; Qing-Zhong Wang; Dai-Zhan Zhou; Xiao-Lan Qin; Jue Ji; Jie Zheng; Hong Chen; Yin Wang; Dao-Ying Geng; Wei-Jun Tang; Chao-Wei Fu; Zhi-Feng Shi; Yi-Chao Zhang; Zhao Ye; Wen-Qiang He; Qi-Lin Zhang; Qi-Sheng Tang; Rong Xie; Jia-Wei Shen; Zu-Jia Wen; Juan Zhou; Tao Wang; Shan Huang; Hui-Jia Qiu; Ni-Dan Qiao; Yi Zhang; Li Pan; Wei-Min Bao; Ying-Chao Liu; Chuan-Xin Huang; Yong-Yong Shi; Yao Zhao
Journal:  Cell Res       Date:  2015-02-13       Impact factor: 25.617

Review 9.  Bilateral inferior petrosal sinus sampling.

Authors:  Benedetta Zampetti; Erika Grossrubatscher; Paolo Dalino Ciaramella; Edoardo Boccardi; Paola Loli
Journal:  Endocr Connect       Date:  2016-06-27       Impact factor: 3.335

10.  Pangenomic Classification of Pituitary Neuroendocrine Tumors.

Authors:  Mario Neou; Chiara Villa; Roberta Armignacco; Anne Jouinot; Marie-Laure Raffin-Sanson; Amandine Septier; Franck Letourneur; Ségolène Diry; Marc Diedisheim; Brigitte Izac; Cassandra Gaspar; Karine Perlemoine; Victoria Verjus; Michèle Bernier; Anne Boulin; Jean-François Emile; Xavier Bertagna; Florence Jaffrezic; Denis Laloe; Bertrand Baussart; Jérôme Bertherat; Stephan Gaillard; Guillaume Assié
Journal:  Cancer Cell       Date:  2019-12-26       Impact factor: 31.743

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  3 in total

Review 1.  Genetic Basis of ACTH-Secreting Adenomas.

Authors:  Pietro Locantore; Rosa Maria Paragliola; Gianluca Cera; Roberto Novizio; Ettore Maggio; Vittoria Ramunno; Andrea Corsello; Salvatore Maria Corsello
Journal:  Int J Mol Sci       Date:  2022-06-19       Impact factor: 6.208

2.  Characterization of Adrenal miRNA-Based Dysregulations in Cushing's Syndrome.

Authors:  Sharmilee Vetrivel; Ru Zhang; Mareen Engel; Andrea Oßwald; Deepika Watts; Alon Chen; Ben Wielockx; Silviu Sbiera; Martin Reincke; Anna Riester
Journal:  Int J Mol Sci       Date:  2022-07-12       Impact factor: 6.208

3.  Difference in miRNA Expression in Functioning and Silent Corticotroph Pituitary Adenomas Indicates the Role of miRNA in the Regulation of Corticosteroid Receptors.

Authors:  Beata J Mossakowska; Paulina Kober; Natalia Rusetska; Joanna Boresowicz; Maria Maksymowicz; Monika Pękul; Grzegorz Zieliński; Andrzej Styk; Jacek Kunicki; Tomasz Mandat; Mateusz Bujko
Journal:  Int J Mol Sci       Date:  2022-03-05       Impact factor: 5.923

  3 in total

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