Chandrashekhar Gendle1, Madhivanan Karthigeyan2, Pravin Salunke1, Kirti Gupta3. 1. Department of Neurosurgery, Postgraduate Institute of Medical Education & Research (PGIMER), Chandigarh, India. 2. Department of Neurosurgery, Postgraduate Institute of Medical Education & Research (PGIMER), Chandigarh, India, karthigeyanm82@gmail.com. 3. Department of Histopathology, PGIMER, Chandigarh, India.
Abstract
INTRODUCTION: Atypical teratoid rhabdoid tumors (ATRT), an uncommon malignant intracranial tumor with aggressive behavior are mostly seen in posterior fossa in young pediatric age-group. CASE PRESENTATION: We present an infrequent location of this tumor in the pineal region in a 5-month-old infant. Also, the lesion was non-enhancing which was highly atypical of an ATRT. It was near-totally excised with the child placed in sitting position. However, within a short interval, a tumor recurrence was noted. CONCLUSION: The case possibly represents an extended spectrum of congenital childhood brain tumors. Importantly, it highlights an atypical imaging of ATRT in very young children.
INTRODUCTION: Atypical teratoid rhabdoid tumors (ATRT), an uncommon malignant intracranial tumor with aggressive behavior are mostly seen in posterior fossa in young pediatric age-group. CASE PRESENTATION: We present an infrequent location of this tumor in the pineal region in a 5-month-old infant. Also, the lesion was non-enhancing which was highly atypical of an ATRT. It was near-totally excised with the child placed in sitting position. However, within a short interval, a tumor recurrence was noted. CONCLUSION: The case possibly represents an extended spectrum of congenital childhood brain tumors. Importantly, it highlights an atypical imaging of ATRT in very young children.