| Literature DB >> 31524317 |
Sandra Mastroianno1, Pietro Palumbo2, Stefano Castellana3, Maria Pia Leone2, Raimondo Massaro1, Domenico Rosario Potenza1, Tommaso Mazza3, Aldo Russo1, Marco Castori2, Massimo Carella2, Giuseppe Di Stolfo1.
Abstract
Cardiomyopathies caused by double gene mutations are rare but conferred a remarkably increased risk of end-stage progression, arrhythmias, and poor outcome. Compound genetic mutations leading to complex phenotype in the setting of cardiomyopathies represent an important challenge in clinical practice, and genetic tests allow risk stratification and personalized clinical management of patients. We report a case of a 50-year-old woman with congestive heart failure characterized by dilated cardiomyopathy, diffuse coronary disease, complete atrioventricular block, and missense mutations in cardiac myosin-binding protein C (MYBPC3) and myopalladin (MYPN). We discuss the plausible role of genetic profile in phenotype determination.Entities:
Keywords: cardiac myosin-binding protein C; complete atrioventricular block; diffuse coronary atherosclerosis; dilated cardiomyopathy; myopalladin
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Year: 2019 PMID: 31524317 PMCID: PMC7358828 DOI: 10.1111/anec.12687
Source DB: PubMed Journal: Ann Noninvasive Electrocardiol ISSN: 1082-720X Impact factor: 1.468