Literature DB >> 3099077

Biosynthesis of peroxisomal beta-oxidation enzymes in infants with Zellweger syndrome.

Y Suzuki, T Orii, T Hashimoto.   

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Year:  1986        PMID： 3099077     DOI： 10.1007/bf01799668

Source DB:  PubMed          Journal:  J Inherit Metab Dis        ISSN： 0141-8955            Impact factor:   4.982


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  10 in total

1.  Peroxisomal and mitochondrial defects in the cerebro-hepato-renal syndrome.

Authors:  S Goldfischer; C L Moore; A B Johnson; A J Spiro; M P Valsamis; H K Wisniewski; R H Ritch; W T Norton; I Rapin; L M Gartner
Journal:  Science       Date:  1973-10-05       Impact factor: 47.728

2.  Purification and properties of carnitine octanoyltransferase and carnitine palmitoyltransferase from rat liver.

Authors:  S Miyazawa; H Ozasa; T Osumi; T Hashimoto
Journal:  J Biochem       Date:  1983-08       Impact factor: 3.387

3.  Cerebro-hepato-renal (Zellweger) syndrome and neonatal adrenoleukodystrophy: similarities in phenotype and accumulation of very long chain fatty acids.

Authors:  F R Brown; A J McAdams; J W Cummins; R Konkol; I Singh; A B Moser; H W Moser
Journal:  Johns Hopkins Med J       Date:  1982-12

4.  Cell-free synthesis and processing of a putative precursor for mitochondrial carbamyl phosphate synthetase I of rat liver.

Authors:  M Mori; S Miura; M Tatibana; P P Cohen
Journal:  Proc Natl Acad Sci U S A       Date:  1979-10       Impact factor: 11.205

5.  Peroxisomal beta-oxidation enzyme proteins in the Zellweger syndrome.

Authors:  J M Tager; W A Van der Beek; R J Wanders; T Hashimoto; H S Heymans; H Van den Bosch; R B Schutgens; A W Schram
Journal:  Biochem Biophys Res Commun       Date:  1985-02-15       Impact factor: 3.575

6.  alpha-Amanitin inhibits the oxidation of long chain fatty acids in mouse liver.

Authors:  T Hashimoto; S Miyazawa; D Gunarso; S Furuta
Journal:  J Biochem       Date:  1981-08       Impact factor: 3.387

7.  Severe plasmalogen deficiency in tissues of infants without peroxisomes (Zellweger syndrome).

Authors:  H S Heymans; R B Schutgens; R Tan; H van den Bosch; P Borst
Journal:  Nature       Date:  1983 Nov 3-9       Impact factor: 49.962

8.  The presence of a new 3-oxoacyl-CoA thiolase in rat liver peroxisomes.

Authors:  S Miyazawa; T Osumi; T Hashimoto
Journal:  Eur J Biochem       Date:  1980-02

9.  Peroxisomal defects in neonatal-onset and X-linked adrenoleukodystrophies.

Authors:  S Goldfischer; J Collins; I Rapin; B Coltoff-Schiller; C H Chang; M Nigro; V H Black; N B Javitt; H W Moser; P B Lazarow
Journal:  Science       Date:  1985-01-04       Impact factor: 47.728

10.  Properties of mitochondria and peroxisomal enoyl-CoA hydratases from rat liver.

Authors:  S Furuta; S Miyazawa; T Osumi; T Hashimoto; N Ui
Journal:  J Biochem       Date:  1980-10       Impact factor: 3.387
  10 in total
  3 in total

1.  Biosynthesis of peroxisomal membrane polypeptides in infants with Zellweger syndrome.

Authors:  Y Suzuki; N Shimozawa; T Orii; J Aikawa; K Tada; T Kuwabara; T Hashimoto
Journal:  J Inherit Metab Dis       Date:  1987       Impact factor: 4.982

Review 2.  On the molecular etiology of decreased arachidonic (20:4n-6), docosapentaenoic (22:5n-6) and docosahexaenoic (22:6n-3) acids in Zellweger syndrome and other peroxisomal disorders.

Authors:  J P Infante; V A Huszagh
Journal:  Mol Cell Biochem       Date:  1997-03       Impact factor: 3.396

Review 3.  Liver pathology and immunocytochemistry in congenital peroxisomal diseases: a review.

Authors:  F Roels; M Espeel; D De Craemer
Journal:  J Inherit Metab Dis       Date:  1991       Impact factor: 4.982
  3 in total

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