Literature DB >> 30275249

Nutritional and Gastrointestinal Management of the Patient With Duchenne Muscular Dystrophy.

David Brumbaugh1, Laura Watne2, Frederic Gottrand3, Ann Gulyas4, Ajay Kaul5, Jacqueline Larson6, Jean Tomezsko7.   

Abstract

Advances in treatment and multidisciplinary management have resulted in improved survival of individuals with Duchenne muscular dystrophy (DMD). Updated DMD treatment recommendations as found in the 2018 DMD Care Considerations are aimed to assist multidisciplinary care teams in providing standardized care to their patients, including attention to nutritional and gastrointestinal health. Challenges remain for care teams in accurately estimating height and nutritional status for individuals with DMD. It can be difficult for patients to maintain a healthy weight. Risk factors for obesity include glucocorticoid therapy and loss of ambulation. In contrast, in the later stages of the disease, swallowing dysfunction can lead to poor nutrition and consideration for gastrostomy tube placement. Constipation is highly prevalent, underrecognized, and undertreated in DMD. With this article, we address the assessment and management of gastrointestinal and nutritional issues, as well as clinical controversies.
Copyright © 2018 by the American Academy of Pediatrics.

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Mesh:

Year:  2018        PMID: 30275249     DOI: 10.1542/peds.2018-0333G

Source DB:  PubMed          Journal:  Pediatrics        ISSN: 0031-4005            Impact factor:   7.124


  3 in total

1.  Adult North Star Network (ANSN): Consensus Guideline For The Standard Of Care Of Adults With Duchenne Muscular Dystrophy.

Authors:  R Quinlivan; B Messer; P Murphy; R Astin; R Mukherjee; J Khan; A Emmanuel; S C Wong; R Kulshresha; T Willis; J Pattni; D Willis; A Morgan; K Savvatis; R Keen; J Bourke; C Marini Bettolo; C Hewamadduma
Journal:  J Neuromuscul Dis       Date:  2021

Review 2.  The Role of Taurine in Skeletal Muscle Functioning and Its Potential as a Supportive Treatment for Duchenne Muscular Dystrophy.

Authors:  Caroline Merckx; Boel De Paepe
Journal:  Metabolites       Date:  2022-02-19

3.  Transition from Childhood to Adulthood in Patients with Duchenne Muscular Dystrophy.

Authors:  Eliza Wasilewska; Sylwia Małgorzewicz; Agnieszka Sobierajska-Rek; Joanna Jabłońska-Brudło; Lucyna Górska; Karolina Śledzińska; Joanna Bautembach-Minkowska; Jolanta Wierzba
Journal:  Medicina (Kaunas)       Date:  2020-08-24       Impact factor: 2.430

  3 in total

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