Literature DB >> 29596760

Precision Modeling of Pulmonary Hypertension Pathology with Induced Pluripotent Stem Cell-derived Cells.

James D West1, Erica J Carrier1.   

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Year:  2018        PMID: 29596760      PMCID: PMC6058992          DOI: 10.1164/rccm.201803-0480ED

Source DB:  PubMed          Journal:  Am J Respir Crit Care Med        ISSN: 1073-449X            Impact factor:   21.405


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  9 in total

Review 1.  Redox biology in pulmonary arterial hypertension (2013 Grover Conference Series).

Authors:  Joshua P Fessel; James D West
Journal:  Pulm Circ       Date:  2015-12       Impact factor: 3.017

2.  Patient-Specific iPSC-Derived Endothelial Cells Uncover Pathways that Protect against Pulmonary Hypertension in BMPR2 Mutation Carriers.

Authors:  Mingxia Gu; Ning-Yi Shao; Silin Sa; Dan Li; Vittavat Termglinchan; Mohamed Ameen; Ioannis Karakikes; Gustavo Sosa; Fabian Grubert; Jaecheol Lee; Aiqin Cao; Shalina Taylor; Yu Ma; Zhixin Zhao; James Chappell; Rizwan Hamid; Eric D Austin; Joseph D Gold; Joseph C Wu; Michael P Snyder; Marlene Rabinovitch
Journal:  Cell Stem Cell       Date:  2016-12-22       Impact factor: 24.633

3.  Contributions of BMPR2 Mutations and Extrinsic Factors to Cellular Phenotypes of Pulmonary Arterial Hypertension Revealed by Induced Pluripotent Stem Cell Modeling.

Authors:  Fedir N Kiskin; C-Hong Chang; Christopher J Z Huang; Baraa Kwieder; Christine Cheung; Benjamin J Dunmore; Felipe Serrano; Sanjay Sinha; Nicholas W Morrell; Amer A Rana
Journal:  Am J Respir Crit Care Med       Date:  2018-07-15       Impact factor: 21.405

4.  Induced Pluripotent Stem Cell Model of Pulmonary Arterial Hypertension Reveals Novel Gene Expression and Patient Specificity.

Authors:  Silin Sa; Mingxia Gu; James Chappell; Ning-Yi Shao; Mohamed Ameen; Kathryn A T Elliott; Dan Li; Fabian Grubert; Caiyun G Li; Shalina Taylor; Aiqin Cao; Yu Ma; Ryan Fong; Long Nguyen; Joseph C Wu; Michael P Snyder; Marlene Rabinovitch
Journal:  Am J Respir Crit Care Med       Date:  2017-04-01       Impact factor: 21.405

5.  BMPR2 preserves mitochondrial function and DNA during reoxygenation to promote endothelial cell survival and reverse pulmonary hypertension.

Authors:  Isabel Diebold; Jan K Hennigs; Kazuya Miyagawa; Caiyun G Li; Nils P Nickel; Mark Kaschwich; Aiqin Cao; Lingli Wang; Sushma Reddy; Pin-I Chen; Kiichi Nakahira; Miguel A Alejandre Alcazar; Rachel K Hopper; Lijuan Ji; Brian J Feldman; Marlene Rabinovitch
Journal:  Cell Metab       Date:  2015-04-07       Impact factor: 27.287

Review 6.  Mitochondrial dynamics in pulmonary arterial hypertension.

Authors:  John Ryan; Asish Dasgupta; Jessica Huston; Kuang-Huieh Chen; Stephen L Archer
Journal:  J Mol Med (Berl)       Date:  2015-02-13       Impact factor: 4.599

7.  Enhancing Insights into Pulmonary Vascular Disease through a Precision Medicine Approach. A Joint NHLBI-Cardiovascular Medical Research and Education Fund Workshop Report.

Authors:  John H Newman; Stuart Rich; Steven H Abman; John H Alexander; John Barnard; Gerald J Beck; Raymond L Benza; Todd M Bull; Stephen Y Chan; Hyung J Chun; Declan Doogan; Jocelyn Dupuis; Serpil C Erzurum; Robert P Frantz; Mark Geraci; Hunter Gillies; Mark Gladwin; Michael P Gray; Anna R Hemnes; Roy S Herbst; Adrian F Hernandez; Nicholas S Hill; Evelyn M Horn; Kendall Hunter; Zhi-Cheng Jing; Roger Johns; Sanjay Kaul; Steven M Kawut; Tim Lahm; Jane A Leopold; Greg D Lewis; Stephen C Mathai; Vallerie V McLaughlin; Evangelos D Michelakis; Steven D Nathan; William Nichols; Grier Page; Marlene Rabinovitch; Jonathan Rich; Franz Rischard; Sharon Rounds; Sanjiv J Shah; Victor F Tapson; Naomi Lowy; Norman Stockbridge; Gail Weinmann; Lei Xiao
Journal:  Am J Respir Crit Care Med       Date:  2017-06-15       Impact factor: 21.405

8.  Mitochondrial hyperpolarization in pulmonary vascular remodeling. Mitochondrial uncoupling protein deficiency as disease model.

Authors:  Oleg Pak; Natascha Sommer; Timm Hoeres; Adel Bakr; Sharon Waisbrod; Akylbek Sydykov; Daniela Haag; Azadeh Esfandiary; Baktybek Kojonazarov; Florian Veit; Beate Fuchs; Friederike Christine Weisel; Matthias Hecker; Ralph Theo Schermuly; Friedrich Grimminger; Hossein Ardeschir Ghofrani; Werner Seeger; Norbert Weissmann
Journal:  Am J Respir Cell Mol Biol       Date:  2013-09       Impact factor: 6.914

9.  Dysfunctional BMPR2 signaling drives an abnormal endothelial requirement for glutamine in pulmonary arterial hypertension.

Authors:  Robert A Egnatchik; Evan L Brittain; Amy T Shah; Wassim H Fares; H James Ford; Ken Monahan; Christie J Kang; Emily G Kocurek; Shijun Zhu; Thong Luong; Thuy T Nguyen; Erik Hysinger; Eric D Austin; Melissa C Skala; Jamey D Young; L Jackson Roberts; Anna R Hemnes; James West; Joshua P Fessel
Journal:  Pulm Circ       Date:  2017-02-01       Impact factor: 3.017

  9 in total

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