Literature DB >> 29067636

A novel finding of Rapunzel syndrome.

Itaru Iwama1, Ryusuke Nambu2, Tomoko Hara2.   

Abstract

Rapunzel syndrome is a rare form of gastric trichobezoar (hair ball) involving extension of a tail of the hair into the small bowel. A 13-year-old girl was admitted with a 4-day history of epigastric pain and nausea which worsened after meals. Abdominal ultrasound showed duodenal wall thickening and lymphadenopathy. Esophagogastroduodenoscopy identified a gastric trichobezoar with a tail extending into the duodenum. In addition, multiple longitudinal duodenal and jejunal ulcers were noted. The ulcers appeared to be a result of direct pressure by the tail itself against the intestinal mucosa. The trichobezoar was successfully retrieved endoscopically under general anesthesia. Her symptoms resolved completely after retrieval. Psychiatric follow-up was carried out to help reduce the risk of recurrence. Here, we describe a novel complication of Rapunzel syndrome, i.e., multiple longitudinal ulcers of the small intestine. This novel finding suggests that the mucosal damage caused by the trichobezoar of Rapunzel syndrome can occur in an earlier stage than previously thought. In addition, we also strongly recommend using general anesthesia with intubation when removing a gastric trichobezoar to ensure protection of the airway.

Entities:  

Keywords:  Dudenal ulcer; Jejunal ulcer; Longitudinal ulcer; Rapunzel syndrome; Trichobezoar

Mesh:

Year:  2017        PMID: 29067636     DOI: 10.1007/s12328-017-0790-8

Source DB:  PubMed          Journal:  Clin J Gastroenterol        ISSN: 1865-7265


  15 in total

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Authors:  C T Wai; G Lau; D S Sutedja
Journal:  Singapore Med J       Date:  2005-07       Impact factor: 1.858

2.  Endoscopic removal of a gastric trichobezoar in a pediatric patient.

Authors:  Ahmet Aybar; Anca M Safta
Journal:  Gastrointest Endosc       Date:  2011-01-26       Impact factor: 9.427

3.  Recurrent Rapunzel syndrome.

Authors:  S K Tiwary; S Kumar; R Khanna; A K Khanna
Journal:  Singapore Med J       Date:  2011-06       Impact factor: 1.858

4.  Endoscopic retrieval of a gastric trichobezoar.

Authors:  Hironori Konuma; Kuangi Fu; Takashi Morimoto; Takayoshi Shimizu; Yuko Izumi; Satoko Shiyanagi; Masahiko Urao; Akihisa Miyazaki; Sumio Watanabe
Journal:  World J Gastrointest Endosc       Date:  2011-01-16

5.  Rapunzel syndrome with a fatal outcome in a neglected child.

Authors:  Denise Estefan Ventura; Fernando A Mardiros Herbella; Sergio T Schettini; Carlos Delmonte
Journal:  J Pediatr Surg       Date:  2005-10       Impact factor: 2.545

Review 6.  Management of trichobezoar: case report and literature review.

Authors:  R R Gorter; C M F Kneepkens; E C J L Mattens; D C Aronson; H A Heij
Journal:  Pediatr Surg Int       Date:  2010-03-06       Impact factor: 1.827

7.  An unusual cause of postfundoplication vomiting.

Authors:  Sonia Michail; Vivian Nanagas; Adam G Mezoff
Journal:  J Pediatr Surg       Date:  2008-03       Impact factor: 2.545

8.  Endoscopic management of huge bezoars.

Authors:  Y G Wang; U Seitz; Z L Li; N Soehendra; X A Qiao
Journal:  Endoscopy       Date:  1998-05       Impact factor: 10.093

9.  An unusual cause of gastric perforation in childhood: trichobezoar (Rapunzel syndrome). A case report.

Authors:  Orhan Koç; Fesih Doğan Yildiz; Adnan Narci; Tolga Altuğ Sen
Journal:  Eur J Pediatr       Date:  2008-06-12       Impact factor: 3.183

10.  Endoscopic retrieval of gastric trichophytobezoar: Case report of a 12-year-old girl with trichophagia.

Authors:  Jiu-Ling Zhao; Wei-Chuan Zhao; Yu-Shui Wang
Journal:  Medicine (Baltimore)       Date:  2017-01       Impact factor: 1.889

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  1 in total

1.  Rapunzel Syndrome.

Authors:  Kumble Seetharama Madhusudhan; Manas Vaishnav; Danny Joy
Journal:  J Gastrointest Surg       Date:  2022-01-07       Impact factor: 3.452

  1 in total

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