| Literature DB >> 28936439 |
Pranav Sharma1, Puneet Kochar1, Salil Sharma1, Nishant Gupta2, Shuo Li1, Kusum Hooda1, Yogesh Kumar1.
Abstract
Pulmonary arterio-venous malformations (PAVMs) are abnormal pulmonary arteries and pulmonary veins communicating directly without interposition of a capillary bed and about 80-90% of patients with PAVMs eventually may present with hereditary hemorrhagic telangiectasia (HHT), remaining ones are sporadic cases. On the other hand, about 15-35% of HHT patients may present with PAVMs. The PAVMs have a tendency to grow and increase in size over time and various factors like puberty, pregnancy and pulmonary arterial hypertension (PAH) affect growth. This condition needs early diagnosis, aggressive management and vigilant follow up. Our article aims to review pulmonary AVMs as a rare cause of strokes in young patients. We will discuss the clinical presentation, diagnosis, complications, the therapeutic options and the follow up.Entities:
Keywords: Pulmonary arterio-venous malformation (PAVMs); cerebral ischemia; hereditary hemorrhagic telangiectasia (HHT); transcatheter embolization
Year: 2017 PMID: 28936439 PMCID: PMC5599280 DOI: 10.21037/atm.2017.06.23
Source DB: PubMed Journal: Ann Transl Med ISSN: 2305-5839