| Literature DB >> 27408442 |
Ramya Uppuluri1, Vimal Kumar1, Deenadayalan Munirathnam1, Hemalatha Doss1, Sreejith Ramachandrakurup1, Divya Subburaj1, Revathi Raj1.
Abstract
Kaposiform hemangioendothelioma is a rare, highly vascular and aggressive soft tissue tumor frequently associated with Kasabach-Merritt phenomenon, usually seen in early infancy. Early diagnosis by means of MRI and tissue biopsy portends a better outcome. Treatment includes surgical excision when feasible and medical management with steroids, propranolol, vincristine and supportive treatment for coagulopathy. We report a 3 months old female infant who was diagnosed, treated successfully and is now in complete remission.Entities:
Keywords: Kaposiform hemangioendothelioma; Kasabach–Merritt phenomenon; Remission; Steroids; Vascular soft tissue tumor; Vincristine
Year: 2016 PMID: 27408442 PMCID: PMC4925564 DOI: 10.1007/s12288-016-0674-y
Source DB: PubMed Journal: Indian J Hematol Blood Transfus ISSN: 0971-4502 Impact factor: 0.900