Literature DB >> 26857763

Epidemiology of Cystic Fibrosis.

Kimberly A Spoonhower1, Pamela B Davis2.   

Abstract

Improved quality of care and rapidly emerging therapeutic strategies to restore chloride transport profoundly impact the epidemiology and pathobiology of cystic fibrosis (CF) in the twenty-first century. CF now serves as a model for chronic illness management, continuous quality improvement via registry data, and a seamless link between basic science research, translational studies, clinical trials, and outcomes research to enable rapid expansion of treatment options.
Copyright © 2016 Elsevier Inc. All rights reserved.

Entities:  

Keywords:  Cystic fibrosis; Cystic fibrosis diagnosis; Cystic fibrosis epidemiology; Review

Mesh:

Year:  2016        PMID: 26857763     DOI: 10.1016/j.ccm.2015.10.002

Source DB:  PubMed          Journal:  Clin Chest Med        ISSN: 0272-5231            Impact factor:   2.878


  32 in total

1.  Plasma metabolomics in adults with cystic fibrosis during a pulmonary exacerbation: A pilot randomized study of high-dose vitamin D3 administration.

Authors:  Jessica A Alvarez; Elizabeth Y Chong; Douglas I Walker; Joshua D Chandler; Ellen S Michalski; Ruth E Grossmann; Karan Uppal; Shuzhao Li; Jennifer K Frediani; Rabindra Tirouvanziam; ViLinh T Tran; Vin Tangpricha; Dean P Jones; Thomas R Ziegler
Journal:  Metabolism       Date:  2017-02-11       Impact factor: 8.694

Review 2.  DENTAL ENAMEL FORMATION AND IMPLICATIONS FOR ORAL HEALTH AND DISEASE.

Authors:  Rodrigo S Lacruz; Stefan Habelitz; J Timothy Wright; Michael L Paine
Journal:  Physiol Rev       Date:  2017-07-01       Impact factor: 37.312

3.  Nationwide trends of hospitalizations for cystic fibrosis in the United States from 2003 to 2013.

Authors:  Abhinav Agrawal; Abhishek Agarwal; Dhruv Mehta; Rutuja R Sikachi; Doantrang Du; Janice Wang
Journal:  Intractable Rare Dis Res       Date:  2017-08

Review 4.  Cystic Fibrosis and Pseudomonas aeruginosa: the Host-Microbe Interface.

Authors:  Sankalp Malhotra; Don Hayes; Daniel J Wozniak
Journal:  Clin Microbiol Rev       Date:  2019-05-29       Impact factor: 26.132

Review 5.  Gene Editing and Genetic Lung Disease. Basic Research Meets Therapeutic Application.

Authors:  Deepthi Alapati; Edward E Morrisey
Journal:  Am J Respir Cell Mol Biol       Date:  2017-03       Impact factor: 6.914

6.  In utero gene editing for monogenic lung disease.

Authors:  Deepthi Alapati; William J Zacharias; Heather A Hartman; Avery C Rossidis; John D Stratigis; Nicholas J Ahn; Barbara Coons; Su Zhou; Hiaying Li; Kshitiz Singh; Jeremy Katzen; Yaniv Tomer; Alexandra C Chadwick; Kiran Musunuru; Michael F Beers; Edward E Morrisey; William H Peranteau
Journal:  Sci Transl Med       Date:  2019-04-17       Impact factor: 17.956

Review 7.  Meconium Ileus.

Authors:  John H T Waldhausen; Morgan Richards
Journal:  Clin Colon Rectal Surg       Date:  2018-02-25

8.  Impact of social complexity on outcomes in cystic fibrosis after transfer to adult care.

Authors:  Erin M Crowley; Gabriel T Bosslet; Babar Khan; Mary Ciccarelli; Cynthia D Brown
Journal:  Pediatr Pulmonol       Date:  2018-04-02

9.  Cystic Fibrosis Related Diabetes: a Unique Challenge in Diabetes Care.

Authors:  Marina Litvin; Schola Nwachukwu
Journal:  Mo Med       Date:  2016 Sep-Oct

Review 10.  A Review of Trikafta: Triple Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Modulator Therapy.

Authors:  Anas Zaher; Jude ElSaygh; Dalal Elsori; Hassan ElSaygh; Abdulsabar Sanni
Journal:  Cureus       Date:  2021-07-03
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