Literature DB >> 25607428

Origins of cystic fibrosis lung disease.

David A Stoltz, David K Meyerholz, Michael J Welsh.   

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Year:  2015        PMID： 25607428      PMCID： PMC4916857          DOI： 10.1056/NEJMra1300109

Source DB:  PubMed          Journal:  N Engl J Med        ISSN： 0028-4793            Impact factor:   91.245


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  72 in total

Review 1.  Submucosal glands and airway defense.

Authors:  Jeffrey J Wine; Nam Soo Joo
Journal:  Proc Am Thorac Soc       Date:  2004

Review 2.  Role of airway surface liquid and submucosal glands in cystic fibrosis lung disease.

Authors:  A S Verkman; Yuanlin Song; Jay R Thiagarajah
Journal:  Am J Physiol Cell Physiol       Date:  2003-01       Impact factor: 4.249

3.  Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA.

Authors:  J R Riordan; J M Rommens; B Kerem; N Alon; R Rozmahel; Z Grzelczak; J Zielenski; S Lok; N Plavsic; J L Chou
Journal:  Science       Date:  1989-09-08       Impact factor: 47.728

Review 4.  Does epithelial sodium channel hyperactivity contribute to cystic fibrosis lung disease?

Authors:  Carey A Hobbs; Chong Da Tan; Robert Tarran
Journal:  J Physiol       Date:  2013-07-22       Impact factor: 5.182

5.  Lung disease at diagnosis in infants with cystic fibrosis detected by newborn screening.

Authors:  Peter D Sly; Siobhain Brennan; Catherine Gangell; Nicholas de Klerk; Conor Murray; Lauren Mott; Stephen M Stick; Philip J Robinson; Colin F Robertson; Sarath C Ranganathan
Journal:  Am J Respir Crit Care Med       Date:  2009-04-16       Impact factor: 21.405

6.  Tracheomalacia is associated with lower FEV1 and Pseudomonas acquisition in children with CF.

Authors:  Anthony J Fischer; Sachinkumar B Singh; Ryan J Adam; David A Stoltz; Christopher F Baranano; Simon Kao; Miles M Weinberger; Paul B McCray; Timothy D Starner
Journal:  Pediatr Pulmonol       Date:  2013-10-25

7.  Glycaemic regulation and insulin secretion are abnormal in cystic fibrosis pigs despite sparing of islet cell mass.

Authors:  Aliye Uc; Alicia K Olivier; Michelle A Griffin; David K Meyerholz; Jianrong Yao; Maisam Abu-El-Haija; Katherine M Buchanan; Oriana G Vanegas Calderón; Marwa Abu-El-Haija; Alejandro A Pezzulo; Leah R Reznikov; Mark J Hoegger; Michael V Rector; Lynda S Ostedgaard; Peter J Taft; Nick D Gansemer; Paula S Ludwig; Emma E Hornick; David A Stoltz; Katie L Ode; Michael J Welsh; John F Engelhardt; Andrew W Norris
Journal:  Clin Sci (Lond)       Date:  2015-01       Impact factor: 6.124

8.  Air trapping on chest CT is associated with worse ventilation distribution in infants with cystic fibrosis diagnosed following newborn screening.

Authors:  Graham L Hall; Karla M Logie; Faith Parsons; Sven M Schulzke; Gary Nolan; Conor Murray; Sarath Ranganathan; Phil Robinson; Peter D Sly; Stephen M Stick; Luke Berry; Luke Garratt; John Massie; Lauren Mott; Srinivas Poreddy; Shannon Simpson
Journal:  PLoS One       Date:  2011-08-19       Impact factor: 3.240

9.  Characterization of defects in ion transport and tissue development in cystic fibrosis transmembrane conductance regulator (CFTR)-knockout rats.

Authors:  Katherine L Tuggle; Susan E Birket; Xiaoxia Cui; Jeong Hong; Joe Warren; Lara Reid; Andre Chambers; Diana Ji; Kevin Gamber; Kengyeh K Chu; Guillermo Tearney; Li Ping Tang; James A Fortenberry; Ming Du; Joan M Cadillac; David M Bedwell; Steven M Rowe; Eric J Sorscher; Michelle V Fanucchi
Journal:  PLoS One       Date:  2014-03-07       Impact factor: 3.240

10.  Reduced airway surface pH impairs bacterial killing in the porcine cystic fibrosis lung.

Authors:  Alejandro A Pezzulo; Xiao Xiao Tang; Mark J Hoegger; Mahmoud H Abou Alaiwa; Shyam Ramachandran; Thomas O Moninger; Phillip H Karp; Christine L Wohlford-Lenane; Henk P Haagsman; Martin van Eijk; Botond Bánfi; Alexander R Horswill; David A Stoltz; Paul B McCray; Michael J Welsh; Joseph Zabner
Journal:  Nature       Date:  2012-07-04       Impact factor: 49.962
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  179 in total

1.  Efficient, non-toxic anion transport by synthetic carriers in cells and epithelia.

Authors:  Hongyu Li; Hennie Valkenier; Luke W Judd; Peter R Brotherhood; Sabir Hussain; James A Cooper; Ondřej Jurček; Hazel A Sparkes; David N Sheppard; Anthony P Davis
Journal:  Nat Chem       Date:  2015-11-02       Impact factor: 24.427

Review 2.  Genetically engineered livestock for biomedical models.

Authors:  Christopher S Rogers
Journal:  Transgenic Res       Date:  2016-01-28       Impact factor: 2.788

3.  Single-Cell Transcriptional Archetypes of Airway Inflammation in Cystic Fibrosis.

Authors:  Jonas C Schupp; Sara Khanal; Jose L Gomez; Maor Sauler; Taylor S Adams; Geoffrey L Chupp; Xiting Yan; Sergio Poli; Yujiao Zhao; Ruth R Montgomery; Ivan O Rosas; Charles S Dela Cruz; Emanuela M Bruscia; Marie E Egan; Naftali Kaminski; Clemente J Britto
Journal:  Am J Respir Crit Care Med       Date:  2020-11-15       Impact factor: 21.405

4.  Harnessing the Early-Life Microbiota to Protect Children with Cystic Fibrosis.

Authors:  Leopoldo N Segal; Martin J Blaser
Journal:  J Pediatr       Date:  2015-04-29       Impact factor: 4.406

5.  Acidic Submucosal Gland pH and Elevated Protein Concentration Produce Abnormal Cystic Fibrosis Mucus.

Authors:  Yuliang Xie; Lin Lu; Xiao Xiao Tang; Thomas O Moninger; Tony Jun Huang; David A Stoltz; Michael J Welsh
Journal:  Dev Cell       Date:  2020-07-29       Impact factor: 12.270

6.  Chloride channels regulate differentiation and barrier functions of the mammalian airway.

Authors:  Mu He; Bing Wu; Wenlei Ye; Daniel D Le; Adriane W Sinclair; Valeria Padovano; Yuzhang Chen; Ke-Xin Li; Rene Sit; Michelle Tan; Michael J Caplan; Norma Neff; Yuh Nung Jan; Spyros Darmanis; Lily Yeh Jan
Journal:  Elife       Date:  2020-04-14       Impact factor: 8.140

7.  Control the platelets, control the disease: A novel cystic fibrosis hypothesis.

Authors:  Siobhan Branfield; A Valance Washington
Journal:  J Thromb Haemost       Date:  2020-05-28       Impact factor: 5.824

8.  CFTR gene transfer with AAV improves early cystic fibrosis pig phenotypes.

Authors:  Benjamin Steines; David D Dickey; Jamie Bergen; Katherine Jda Excoffon; John R Weinstein; Xiaopeng Li; Ziying Yan; Mahmoud H Abou Alaiwa; Viral S Shah; Drake C Bouzek; Linda S Powers; Nicholas D Gansemer; Lynda S Ostedgaard; John F Engelhardt; David A Stoltz; Michael J Welsh; Patrick L Sinn; David V Schaffer; Joseph Zabner
Journal:  JCI Insight       Date:  2016-09-08

Review 9.  Autophagy in Pulmonary Diseases.

Authors:  Kiichi Nakahira; Maria Angelica Pabon Porras; Augustine M K Choi
Journal:  Am J Respir Crit Care Med       Date:  2016-11-15       Impact factor: 21.405

10.  Elastase Exocytosis by Airway Neutrophils Is Associated with Early Lung Damage in Children with Cystic Fibrosis.

Authors:  Camilla Margaroli; Luke W Garratt; Hamed Horati; A Susanne Dittrich; Timothy Rosenow; Samuel T Montgomery; Dario L Frey; Milton R Brown; Carsten Schultz; Lokesh Guglani; Anthony Kicic; Limin Peng; Bob J Scholte; Marcus A Mall; Hettie M Janssens; Stephen M Stick; Rabindra Tirouvanziam
Journal:  Am J Respir Crit Care Med       Date:  2019-04-01       Impact factor: 21.405
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