Literature DB >> 25251442

Evaluating Adults With Idiopathic Pancreatitis for Genetic Predisposition: Higher Prevalence of Abnormal Results With Use of Complete Gene Sequencing.

Darren D Ballard1, Joyce R Flueckiger, Evan L Fogel, Lee McHenry, Glen A Lehman, James L Watkins, Stuart Sherman, Gregory A Coté.   

Abstract

OBJECTIVES: In adults with unexplained pancreatitis, the yield of complete gene versus select exosome sequencing on mutation detection and distinguishing clinical characteristics associated with mutations requires clarification. We sought to (1) compare frequency of mutations identified using different techniques and (2) compare clinical characteristics between adults with and without mutations.
METHODS: This is a cohort study of adults with unexplained pancreatitis who underwent genetic testing between January 2008 and December 2012. We compare probabilities of having a positive mutation with complete gene sequencing versus alternatives and describe differences in characteristics among patients with and without mutations.
RESULTS: Of the 370 patients, 67 (18%) had a genetic mutation; 24 (6%) were of high risk. Mutations were significantly more prevalent with use of complete sequencing (42%) versus other approaches (8%, P < 0.0001). Most (44/67, 66%) with a mutation had no family history. Those with high-risk mutations were more likely to have a family history of chronic pancreatitis (21% vs 4%, P = 0.002). Patients with pancreas divisum were more likely to have mutations (27% vs 14%, P = 0.0007).
CONCLUSION: Among individuals with adult-onset pancreatic disease, the probability of finding any mutation, including high risk, is significantly higher using complete gene sequencing. The impact on patients and providers requires further investigation.

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Year:  2015        PMID: 25251442      PMCID: PMC4262640          DOI: 10.1097/MPA.0000000000000225

Source DB:  PubMed          Journal:  Pancreas        ISSN: 0885-3177            Impact factor:   3.327


  40 in total

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Authors:  J P H Drenth; R te Morsche; J B M J Jansen
Journal:  Gut       Date:  2002-05       Impact factor: 23.059

6.  Determination of the relative contribution of three genes-the cystic fibrosis transmembrane conductance regulator gene, the cationic trypsinogen gene, and the pancreatic secretory trypsin inhibitor gene-to the etiology of idiopathic chronic pancreatitis.

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7.  Association of SPINK1 gene mutation and CFTR gene polymorphisms in patients with pancreas divisum presenting with idiopathic pancreatitis.

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8.  Relation between mutations of the cystic fibrosis gene and idiopathic pancreatitis.

Authors:  J A Cohn; K J Friedman; P G Noone; M R Knowles; L M Silverman; P S Jowell
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9.  Mutations of the CFTR gene in pancreatic disease.

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  7 in total

1.  An Evaluation of Factors Associated With Pathogenic PRSS1, SPINK1, CTFR, and/or CTRC Genetic Variants in Patients With Idiopathic Pancreatitis.

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Review 2.  Idiopathic acute pancreatitis: a review on etiology and diagnostic work-up.

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Journal:  Pancreas       Date:  2019-09       Impact factor: 3.327

4.  Genophenotypic Analysis of Pediatric Patients With Acute Recurrent and Chronic Pancreatitis.

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Journal:  Pancreas       Date:  2016-10       Impact factor: 3.327

5.  Hereditary pancreatitis in childhood: course of disease and complications.

Authors:  Regina Prommer; Melanie Kienbauer; Simon Kargl; Rainer Schöfl
Journal:  Wien Klin Wochenschr       Date:  2021-04-28       Impact factor: 1.704

6.  Predictors of Post-Operative Pain Relief in Patients with Chronic Pancreatitis Undergoing the Frey or Whipple Procedure.

Authors:  Amitasha Sinha; Yuval A Patel; Michael Cruise; Karen Matsukuma; Atif Zaheer; Elham Afghani; Dhiraj Yadav; Martin A Makary; Kenzo Hirose; Dana K Andersen; Vikesh K Singh
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7.  Pancreatitis: TIGAR-O Version 2 Risk/Etiology Checklist With Topic Reviews, Updates, and Use Primers.

Authors:  David C Whitcomb
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  7 in total

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