Literature DB >> 24498485

A case of rasmussen encephalitis: the differential diagnoses and role of diagnostic imaging.

Binoj Varghese1, Mk Aneesh2, Navdeep Singh2, Percival Gilwaz3.   

Abstract

Rasmussen encephalitis is an extremely rare chronic inflammatory neurodegenerative disease affecting a single cerebral hemisphere, causing progressive neurological deterioration and intractable seizures. Imaging plays an important role in diagnosis by demonstrating focal or unihemispheric involvement and excluding other possible causes. Here, we report a case of Rasmussen encephalitis with an update on recent diagnostic criteria and emphasis on differential diagnoses which can be excluded on imaging.

Entities:  

Keywords:  Epilepsia partialis continua; Magnetic resonance imaging; Rasmussen encephalitis

Year:  2014        PMID: 24498485      PMCID: PMC3910406          DOI: 10.5001/omj.2014.15

Source DB:  PubMed          Journal:  Oman Med J        ISSN: 1999-768X


  12 in total

1.  Dyke-Davidoff Masson syndrome : neuroimage.

Authors:  D K Kochar; N Jain; B V Sharma; B L Kumawat; C B Meena
Journal:  Neurol India       Date:  2001-12       Impact factor: 2.117

2.  Childhood multiple sclerosis and related disorders.

Authors:  Amna Al-Futaisi
Journal:  Oman Med J       Date:  2007-10

3.  Focal seizures due to chronic localized encephalitis.

Authors:  T RASMUSSEN; J OLSZEWSKI; D LLOYDSMITH
Journal:  Neurology       Date:  1958-06       Impact factor: 9.910

4.  Longitudinal study of MRS metabolites in Rasmussen encephalitis.

Authors:  R M Wellard; R S Briellmann; J C Wilson; R M Kalnins; D P Anderson; P Federico; G C A Fabinyi; I E Scheffer; A S Harvey; G D Jackson
Journal:  Brain       Date:  2004-04-06       Impact factor: 13.501

5.  Diagnosis and staging of Rasmussen's encephalitis by serial MRI and histopathology.

Authors:  C G Bien; H Urbach; M Deckert; J Schramm; O D Wiestler; H Lassmann; C E Elger
Journal:  Neurology       Date:  2002-01-22       Impact factor: 9.910

6.  Neuropathological spectrum of Rasmussen encephalitis.

Authors:  Prabal Deb; Mehar Chand Sharma; Shailesh Gaikwad; Manjari Tripathi; P Sharat Chandra; Satish Jain; Chitra Sarkar
Journal:  Neurol India       Date:  2005-06       Impact factor: 2.117

Review 7.  Pathogenesis, diagnosis and treatment of Rasmussen encephalitis: a European consensus statement.

Authors:  C G Bien; T Granata; C Antozzi; J H Cross; O Dulac; M Kurthen; H Lassmann; R Mantegazza; J-G Villemure; R Spreafico; C E Elger
Journal:  Brain       Date:  2005-02-02       Impact factor: 13.501

8.  Destruction of neurons by cytotoxic T cells: a new pathogenic mechanism in Rasmussen's encephalitis.

Authors:  Christian G Bien; Jan Bauer; Thomas L Deckwerth; Heinz Wiendl; Martina Deckert; Otmar D Wiestler; Johannes Schramm; Christian E Elger; Hans Lassmann
Journal:  Ann Neurol       Date:  2002-03       Impact factor: 10.422

9.  Double pathology in Rasmussen's syndrome: a window on the etiology?

Authors:  Y M Hart; F Andermann; Y Robitaille; K D Laxer; T Rasmussen; R Davis
Journal:  Neurology       Date:  1998-03       Impact factor: 9.910

10.  Autoantibodies to glutamate receptor GluR3 in Rasmussen's encephalitis.

Authors:  S W Rogers; P I Andrews; L C Gahring; T Whisenand; K Cauley; B Crain; T E Hughes; S F Heinemann; J O McNamara
Journal:  Science       Date:  1994-07-29       Impact factor: 47.728

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  4 in total

1.  Refractory Seizure in Childhood: Dyke-Davidoff-Masson Syndrome Revisited.

Authors:  Abhijit Dutta; Sagar Bose; Kaushik Sen; Narayan Pandit; Samarth Sharma
Journal:  Oman Med J       Date:  2016-07

2.  Classical oral manifestations of Dyke-Davidoff-Masson syndrome: a case report with review of the literature.

Authors:  Ritesh Kalaskar; Ashita Ritesh Kalaskar
Journal:  J Korean Assoc Oral Maxillofac Surg       Date:  2018-08-29

3.  A myriad spectrum of seizures on magnetic resonance imaging - A pictorial essay.

Authors:  Rahul Karthik Lingutla; Ajit Mahale; Akshatha R Bhat; Sonali Ullal
Journal:  J Clin Imaging Sci       Date:  2022-01-21

4.  Role of diagnostic imaging in Rasmussen's encephalitis - A case report from Nepal.

Authors:  Suraj Sharma; Prakash Dhakal; Sajiva Aryal; Seema Bhandari; Abhishek Sharma
Journal:  Radiol Case Rep       Date:  2022-07-29
  4 in total

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