| Literature DB >> 15689357 |
C G Bien1, T Granata, C Antozzi, J H Cross, O Dulac, M Kurthen, H Lassmann, R Mantegazza, J-G Villemure, R Spreafico, C E Elger.
Abstract
Rasmussen encephalitis (RE) is a rare but severe immune-mediated brain disorder leading to unilateral hemispheric atrophy, associated progressive neurological dysfunction and intractable seizures. Recent data on the pathogenesis of the disease, its clinical and paraclinical presentation, and therapeutic approaches are summarized. Based on these data, we propose formal diagnostic criteria and a therapeutic pathway for the management of RE patients.Entities:
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Year: 2005 PMID: 15689357 DOI: 10.1093/brain/awh415
Source DB: PubMed Journal: Brain ISSN: 0006-8950 Impact factor: 13.501