Literature DB >> 23572165

A randomized double-blind, placebo-controlled trial of minocycline in children and adolescents with fragile x syndrome.

Mary Jacena S Leigh1, Danh V Nguyen, Yi Mu, Tri I Winarni, Andrea Schneider, Tasleem Chechi, Jonathan Polussa, Paul Doucet, Flora Tassone, Susan M Rivera, David Hessl, Randi J Hagerman.   

Abstract

OBJECTIVE: Minocycline rescued synaptic abnormalities and improved behavior in the fragile X mouse model. Previous open-label human studies demonstrated benefits in individuals with fragile X syndrome (FXS); however, its efficacy in patients with FXS has not been assessed in a controlled trial.
METHOD: Randomized, double-blind, placebo-controlled, crossover trial in individuals with FXS, aged 3.5 years to 16 years (n = 55, mean age 9.2 [SD, 3.6] years). Participants were randomized to minocycline or placebo for 3 months and then switched to the other treatment.
RESULTS: Sixty-nine subjects were screened and 66 were randomized. Fifty-five subjects (83.3%) completed at least the first period and 48 (72.7%) completed the full trial. Intention-to-treat analysis demonstrated significantly greater improvements in one primary outcome, Clinical Global Impression Scale-Improvement after minocycline compared with placebo (2.49 ± 0.13 and 2.97 ± 0.13, respectively, p = .0173) and greater improvement in ad hoc analysis of anxiety and mood-related behaviors on the Visual Analog Scale (minocycline: 5.26 cm ± 0.46 cm, placebo: 4.05 cm ± 0.46 cm; p = .0488). Side effects were not significantly different during the minocycline and placebo treatments. No serious adverse events occurred on minocycline. Results may be potentially biased by study design weaknesses, including unblinding of subjects when they completed the study, drug-related side effects unblinding, and preliminary efficacy analysis results known to investigators.
CONCLUSIONS: Minocycline treatment for 3 months in children with FXS resulted in greater global improvement than placebo. Treatment for 3 months appears safe; however, longer trials are indicated to further assess benefits, side effects, and factors associated with a clinical response to minocycline.

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Year:  2013        PMID: 23572165      PMCID: PMC3706260          DOI: 10.1097/DBP.0b013e318287cd17

Source DB:  PubMed          Journal:  J Dev Behav Pediatr        ISSN: 0196-206X            Impact factor:   2.225


  32 in total

Review 1.  Fragile X syndrome and targeted treatment trials.

Authors:  Randi Hagerman; Julie Lauterborn; Jacky Au; Elizabeth Berry-Kravis
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2.  Minocycline treatment reverses ultrasonic vocalization production deficit in a mouse model of Fragile X Syndrome.

Authors:  Sarah E Rotschafer; Michael S Trujillo; Lorraine E Dansie; Iryna M Ethell; Khaleel A Razak
Journal:  Brain Res       Date:  2011-12-31       Impact factor: 3.252

3.  Epigenetic modification of the FMR1 gene in fragile X syndrome is associated with differential response to the mGluR5 antagonist AFQ056.

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Journal:  Sci Transl Med       Date:  2011-01-05       Impact factor: 17.956

4.  Side effects of minocycline treatment in patients with fragile X syndrome and exploration of outcome measures.

Authors:  Agustini Utari; Weerasak Chonchaiya; Susan M Rivera; Andrea Schneider; Randi J Hagerman; Sultana M H Faradz; Iryna M Ethell; Danh V Nguyen
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5.  Toward the validation of visual analogue scale for anxiety.

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Review 6.  Mechanism-based approaches to treating fragile X.

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9.  FMRP stalls ribosomal translocation on mRNAs linked to synaptic function and autism.

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10.  Neural circuit architecture defects in a Drosophila model of Fragile X syndrome are alleviated by minocycline treatment and genetic removal of matrix metalloproteinase.

Authors:  Saul S Siller; Kendal Broadie
Journal:  Dis Model Mech       Date:  2011-06-13       Impact factor: 5.758

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  94 in total

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Journal:  Curr Pharm Des       Date:  2015       Impact factor: 3.116

Review 2.  Genetic studies in intellectual disability and related disorders.

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Journal:  Nat Rev Genet       Date:  2015-10-27       Impact factor: 53.242

Review 3.  Pharmacological therapies for Angelman syndrome.

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Review 4.  Matrix Metalloproteinase-9 as a Novel Player in Synaptic Plasticity and Schizophrenia.

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Review 5.  Drug discovery for autism spectrum disorder: challenges and opportunities.

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6.  Fragile X syndrome clinical trials: exploring parental decision-making.

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7.  Metformin ameliorates core deficits in a mouse model of fragile X syndrome.

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8.  TARGETED TREATMENTS IN AUTISM AND FRAGILE X SYNDROME.

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Journal:  Res Autism Spectr Disord       Date:  2012-10-01

Review 9.  Drug development for neurodevelopmental disorders: lessons learned from fragile X syndrome.

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Journal:  Nat Rev Drug Discov       Date:  2017-12-08       Impact factor: 84.694

Review 10.  Fragile X syndrome.

Authors:  Wilmar Saldarriaga; Flora Tassone; Laura Yuriko González-Teshima; Jose Vicente Forero-Forero; Sebastián Ayala-Zapata; Randi Hagerman
Journal:  Colomb Med (Cali)       Date:  2014-12-30
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