Literature DB >> 23037928

Management of congenital adrenal hyperplasia in childhood.

Mimi S Kim1, Anna Ryabets-Lienhard, Mitchell E Geffner.   

Abstract

PURPOSE OF REVIEW: Congenital adrenal hyperplasia (CAH) can present management challenges to the pediatric clinician. Glucocorticoid replacement remains the cornerstone of treatment; however, there are new formulations and delivery mechanisms being studied. Clinicians continue to discuss the optimal treatment of patients from the prenatal stage, through infancy to adulthood. As well, the role of genetics in the clinical care of patients with CAH, and screening for complications, remain topics of discussion. This review will highlight advances made in the past year, as they pertain to the management of pediatric patients with CAH. RECENT
FINDINGS: This article covers recent studies pertaining to optimal medication regimens, including prenatal dexamethasone treatment; medication delivery; monitoring of hormonal control; and the role of genotyping and genetics in the management of children with CAH.
SUMMARY: Much remains to be learned about the optimal management of children with CAH, including fludrocortisone replacement in simple-virilizing patients, frequency of specific monitoring strategies (e.g., electrolytes, bone age), catecholamine status, stress-dosing in nonclassical adrenal hyperplasia, and early screening for complications or metabolic sequelae. Further randomized and prospective studies are needed to address these issues.

Entities:  

Mesh:

Substances:

Year:  2012        PMID: 23037928      PMCID: PMC3584711          DOI: 10.1097/MED.0b013e32835a1a1b

Source DB:  PubMed          Journal:  Curr Opin Endocrinol Diabetes Obes        ISSN: 1752-296X            Impact factor:   3.243


  38 in total

1.  Functional studies of CYP21A2 mutants complement structural and clinical predictions of disease severity in CAH.

Authors:  Michela Barbaro; Fernanda C Soardi; Maricilda Palandi de Mello; Anna Wedell; Svetlana Lajic
Journal:  Clin Endocrinol (Oxf)       Date:  2012-05       Impact factor: 3.478

2.  Adrenal gland: New dual-release hydrocortisone tablet for adrenal insufficiency.

Authors:  Joana Osório
Journal:  Nat Rev Endocrinol       Date:  2011-12-13       Impact factor: 43.330

3.  Rapid steroid hormone quantification for congenital adrenal hyperplasia (CAH) in dried blood spots using UPLC liquid chromatography-tandem mass spectrometry.

Authors:  Nils Janzen; Stefanie Sander; Michael Terhardt; Ulrike Steuerwald; Michael Peter; Anibh M Das; Johannes Sander
Journal:  Steroids       Date:  2011-08-02       Impact factor: 2.668

4.  Efficiency of neonatal screening for congenital adrenal hyperplasia due to 21-hydroxylase deficiency in children born in mainland France between 1996 and 2003.

Authors:  Bénédicte Coulm; Joel Coste; Véronique Tardy; Emmanuel Ecosse; Michel Roussey; Yves Morel; Jean-Claude Carel
Journal:  Arch Pediatr Adolesc Med       Date:  2012-02

5.  Improved cortisol exposure-time profile and outcome in patients with adrenal insufficiency: a prospective randomized trial of a novel hydrocortisone dual-release formulation.

Authors:  G Johannsson; A G Nilsson; R Bergthorsdottir; P Burman; P Dahlqvist; B Ekman; B E Engström; T Olsson; O Ragnarsson; M Ryberg; J Wahlberg; B M K Biller; J P Monson; P M Stewart; H Lennernäs; S Skrtic
Journal:  J Clin Endocrinol Metab       Date:  2011-11-23       Impact factor: 5.958

6.  Steroid 21-hydroxylase gene mutational spectrum in 454 Argentinean patients: genotype-phenotype correlation in a large cohort of patients with congenital adrenal hyperplasia.

Authors:  Roxana Marino; Pablo Ramirez; Jesica Galeano; Natalia Perez Garrido; Carlos Rocco; Marta Ciaccio; Diana M Warman; Gabriela Guercio; Eduardo Chaler; Mercedes Maceiras; Ignacio Bergadá; Mirta Gryngarten; Viviana Balbi; Esther Pardes; Marco A Rivarola; Alicia Belgorosky
Journal:  Clin Endocrinol (Oxf)       Date:  2011-10       Impact factor: 3.478

7.  Absence of clinically relevant growth acceleration in untreated children with non-classical congenital adrenal hyperplasia.

Authors:  Karijn J Pijnenburg-Kleizen; George F Borm; Barto J Otten; Dina A Schott; Erica L van den Akker; Wilhelmina H Stokvis-Brantsma; Paul G Voorhoeve; Boudewijn Bakker; Hedi L Claahsen-van der Grinten
Journal:  Horm Res Paediatr       Date:  2012-04-12       Impact factor: 2.852

Review 8.  Optimal glucocorticoid therapy.

Authors:  Miguel Debono; Richard J Ross
Journal:  Endocr Dev       Date:  2010-12-16

9.  Correlation between androstenedione and 17-hydroxyprogesterone levels in the saliva and plasma of patients with congenital adrenal hyperplasia.

Authors:  A Z Juniarto; K Goossens; B A Setyawati; S L Drop; F H de Jong; S M H Faradz
Journal:  Singapore Med J       Date:  2011-11       Impact factor: 1.858

10.  Growth patterns in the first three years of life in children with classical congenital adrenal hyperplasia diagnosed by newborn screening and treated with low doses of hydrocortisone.

Authors:  W Bonfig; H Schmidt; H P Schwarz
Journal:  Horm Res Paediatr       Date:  2010-08-12       Impact factor: 2.852

View more
  5 in total

Review 1.  Management of Childhood Congenital Adrenal Hyperplasia-An Integrative Review of the Literature.

Authors:  Louise Fleming; Marcia Van Riper; Kathleen Knafl
Journal:  J Pediatr Health Care       Date:  2017-04-13       Impact factor: 1.812

2.  Low Adrenomedullary Function Predicts Acute Illness in Infants With Classical Congenital Adrenal Hyperplasia.

Authors:  Jonathan Weber; Veeraya K Tanawattanacharoen; Amy Seagroves; Mark C Liang; Christina M Koppin; Heather M Ross; Tania A S S Bachega; Mitchell E Geffner; Monica Serrano-Gonzalez; Gagandeep Bhullar; Mimi S Kim
Journal:  J Clin Endocrinol Metab       Date:  2022-01-01       Impact factor: 6.134

Review 3.  Non-Classic Disorder of Adrenal Steroidogenesis and Clinical Dilemmas in 21-Hydroxylase Deficiency Combined with Backdoor Androgen Pathway. Mini-Review and Case Report.

Authors:  Marta Sumińska; Klaudia Bogusz-Górna; Dominika Wegner; Marta Fichna
Journal:  Int J Mol Sci       Date:  2020-06-29       Impact factor: 5.923

4.  Adrenal Insufficiency in Young Children: a Mixed Methods Study of Parents' Experiences.

Authors:  Amy Simpson; Richard Ross; John Porter; Simon Dixon; Martin J Whitaker; Amy Hunter
Journal:  J Genet Couns       Date:  2018-07-07       Impact factor: 2.537

5.  White Matter Microstructural Differences in Youth With Classical Congenital Adrenal Hyperplasia.

Authors:  Devyn L Cotter; Anisa Azad; Ryan P Cabeen; Mimi S Kim; Mitchell E Geffner; Farshid Sepehrband; Megan M Herting
Journal:  J Clin Endocrinol Metab       Date:  2021-10-21       Impact factor: 6.134

  5 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.