Literature DB >> 22461476

Decreased hepcidin expression in murine β-thalassemia is associated with suppression of Bmp/Smad signaling.

Nermi L Parrow, Sara Gardenghi, Pedro Ramos, Carla Casu, Robert W Grady, Erik R Anderson, Yatrik M Shah, Huihui Li, Yelena Z Ginzburg, Robert E Fleming, Stefano Rivella.   

Abstract

Entities:  

Mesh:

Substances:

Year:  2012        PMID: 22461476     DOI: 10.1182/blood-2012-01-405563

Source DB:  PubMed          Journal:  Blood        ISSN: 0006-4971            Impact factor:   22.113


× No keyword cloud information.
  14 in total

1.  Combination of Tmprss6- ASO and the iron chelator deferiprone improves erythropoiesis and reduces iron overload in a mouse model of beta-thalassemia intermedia.

Authors:  Carla Casu; Mariam Aghajan; Paraskevi Rea Oikonomidou; Shuling Guo; Brett P Monia; Stefano Rivella
Journal:  Haematologica       Date:  2015-09-24       Impact factor: 9.941

2.  Hepcidin suppression in β-thalassemia is associated with the down-regulation of atonal homolog 8.

Authors:  Supranee Upanan; Andrew T McKie; Gladys O Latunde-Dada; Sittiruk Roytrakul; Chairat Uthaipibull; Peraphan Pothacharoen; Prachya Kongtawelert; Suthat Fucharoen; Somdet Srichairatanakool
Journal:  Int J Hematol       Date:  2017-04-12       Impact factor: 2.490

Review 3.  Iron metabolism under conditions of ineffective erythropoiesis in β-thalassemia.

Authors:  Stefano Rivella
Journal:  Blood       Date:  2018-11-06       Impact factor: 22.113

Review 4.  Gene Addition Strategies for β-Thalassemia and Sickle Cell Anemia.

Authors:  Alisa C Dong; Stefano Rivella
Journal:  Adv Exp Med Biol       Date:  2017       Impact factor: 2.622

5.  Minihepcidin peptides as disease modifiers in mice affected by β-thalassemia and polycythemia vera.

Authors:  Carla Casu; Paraskevi Rea Oikonomidou; Huiyong Chen; Vijay Nandi; Yelena Ginzburg; Princy Prasad; Robert E Fleming; Yatrik M Shah; Erika V Valore; Elizabeta Nemeth; Tomas Ganz; Brian MacDonald; Stefano Rivella
Journal:  Blood       Date:  2016-05-06       Impact factor: 22.113

6.  Smad1/5 is required for erythropoietin-mediated suppression of hepcidin in mice.

Authors:  Chia-Yu Wang; Amanda B Core; Susanna Canali; Kimberly B Zumbrennen-Bullough; Sinan Ozer; Lieve Umans; An Zwijsen; Jodie L Babitt
Journal:  Blood       Date:  2017-04-24       Impact factor: 22.113

7.  Reducing TMPRSS6 ameliorates hemochromatosis and β-thalassemia in mice.

Authors:  Shuling Guo; Carla Casu; Sara Gardenghi; Sheri Booten; Mariam Aghajan; Raechel Peralta; Andy Watt; Sue Freier; Brett P Monia; Stefano Rivella
Journal:  J Clin Invest       Date:  2013-03-25       Impact factor: 14.808

8.  The murine growth differentiation factor 15 is not essential for systemic iron homeostasis in phlebotomized mice.

Authors:  Guillem Casanovas; Maja Vujić Spasic; Carla Casu; Stefano Rivella; Jens Strelau; Klaus Unsicker; Martina U Muckenthaler
Journal:  Haematologica       Date:  2012-09-14       Impact factor: 9.941

9.  Increased hepcidin in transferrin-treated thalassemic mice correlates with increased liver BMP2 expression and decreased hepatocyte ERK activation.

Authors:  Huiyong Chen; Tenzin Choesang; Huihui Li; Shuming Sun; Petra Pham; Weili Bao; Maria Feola; Mark Westerman; Guiyuan Li; Antonia Follenzi; Lionel Blanc; Stefano Rivella; Robert E Fleming; Yelena Z Ginzburg
Journal:  Haematologica       Date:  2015-12-03       Impact factor: 9.941

Review 10.  What can we learn from ineffective erythropoiesis in thalassemia?

Authors:  Paraskevi Rea Oikonomidou; Stefano Rivella
Journal:  Blood Rev       Date:  2017-10-03       Impact factor: 8.250

View more

北京卡尤迪生物科技股份有限公司 © 2022-2023.