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Literature DB >> 21183701

Platelet secretion defect in patients with familial hemophagocytic lymphohistiocytosis type 5 (FHL-5).

Kirstin Sandrock, Lea Nakamura, Thomas Vraetz, Karin Beutel, Stephan Ehl, Barbara Zieger.

Abstract

Entities: Disease Species

Mesh：

Substances：
Hemostatics
Thrombin

Year: 2010 PMID： 21183701 DOI： 10.1182/blood-2010-08-302943

Source DB: PubMed Journal: Blood ISSN： 0006-4971 Impact factor: 22.113

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Cited

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13 in total

1. Munc18-2, but not Munc18-1 or Munc18-3, regulates platelet exocytosis, hemostasis, and thrombosis.

Authors: Eduardo I Cardenas; Ricardo Gonzalez; Keegan Breaux; Qi Da; Berenice A Gutierrez; Marco A Ramos; Rodolfo A Cardenas; Alan R Burns; Rolando E Rumbaut; Roberto Adachi
Journal: J Biol Chem Date: 2019-01-29 Impact factor: 5.157

Review 2. How I treat hemophagocytic lymphohistiocytosis.

Authors: Michael B Jordan; Carl E Allen; Sheila Weitzman; Alexandra H Filipovich; Kenneth L McClain
Journal: Blood Date: 2011-08-09 Impact factor: 22.113

3. Syntaxin-11, but not syntaxin-2 or syntaxin-4, is required for platelet secretion.

Authors: Shaojing Ye; Zubair A Karim; Rania Al Hawas; Jeffery E Pessin; Alexandra H Filipovich; Sidney W Whiteheart
Journal: Blood Date: 2012-07-05 Impact factor: 22.113

4. Platelet-derived immune-modulatory mediators and transfusion: time to consider their effects?

Authors: Fabrice Cognasse; Hind Hamzeh-Cognasse
Journal: Blood Transfus Date: 2022-03-09 Impact factor: 5.752

5. Disrupted apical exocytosis of cargo vesicles causes enteropathy in FHL5 patients with Munc18-2 mutations.

Authors: Georg F Vogel; Jorik M van Rijn; Iris M Krainer; Andreas R Janecke; Carsten Posovszky; Marta Cohen; Claire Searle; Prevost Jantchou; Johanna C Escher; Natalie Patey; Ernest Cutz; Thomas Müller; Sabine Middendorp; Michael W Hess; Lukas A Huber
Journal: JCI Insight Date: 2017-07-20

Platelet secretion defect in patients with familial hemophagocytic lymphohistiocytosis type 5 (FHL-5).

1. Munc18-2, but not Munc18-1 or Munc18-3, regulates platelet exocytosis, hemostasis, and thrombosis.

Review 2. How I treat hemophagocytic lymphohistiocytosis.

3. Syntaxin-11, but not syntaxin-2 or syntaxin-4, is required for platelet secretion.

4. Platelet-derived immune-modulatory mediators and transfusion: time to consider their effects?

5. Disrupted apical exocytosis of cargo vesicles causes enteropathy in FHL5 patients with Munc18-2 mutations.

6. Platelet secretion and hemostasis require syntaxin-binding protein STXBP5.

7. Hemophagocytic Lymphohistiocytosis Masquerading as Acute Liver Failure: A Single Center Experience.

8. Munc18b/STXBP2 is required for platelet secretion.

Review 9. Familial hemophagocytic lymphohistiocytosis: when rare diseases shed light on immune system functioning.

10. Graded defects in cytotoxicity determine severity of hemophagocytic lymphohistiocytosis in humans and mice.