| Literature DB >> 19564750 |
Vilmarie Rodriguez1, Adrianna Lee, Patricia M Witman, Peter A Anderson.
Abstract
Kasabach-Merritt phenomenon (KMP) is a rare thrombocytopenic consumption coagulopathy associated with an enlarging tufted angioma or kaposiform hemangioendothelioma. We report a case series of patients with KMP and discuss the treatment options and outcomes. Nine patients with a diagnosis of KMP were identified through retrospective chart review-6 had "definite KMP" and 3 had "less likely KMP." The hematologic features of KMP and those of chronic coagulopathy seen with other vascular malformations can be similar, which makes KMP difficult to distinguish.Entities:
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Year: 2009 PMID: 19564750 DOI: 10.1097/MPH.0b013e3181a71830
Source DB: PubMed Journal: J Pediatr Hematol Oncol ISSN: 1077-4114 Impact factor: 1.289