Literature DB >> 19175930

Oculopharyngeal muscular dystrophy as a rare differential diagnosis for unexplained dysphagia: a case report.

Klaus Bumm1, Martin Zenker, Alessandro Bozzato.   

Abstract

INTRODUCTION: We wish to report on a rare cause of dysphagia; oculopharyngeal muscular dystrophy (OPMD). It is a late adult onset autosomal dominant form of muscular dystrophy that constitutes as a rare diagnosis for any place outside of Canada and first case in southern Germany. CASE
PRESENTATION: We report the medical odyssey of a 57-year old male Caucasian patient. He was referred at our hospital for further clarification of a progressive dysphagia, which, at first view, was thought to be tumor related due to the patient's typical anamnesis.
CONCLUSION: The present report outlines the importance of considering this rare disease for general medicine practitioners as well as head and neck specialists as a differential diagnosis for swallowing disorders with, even at second view, uncertain cause.

Entities:  

Year:  2009        PMID: 19175930      PMCID: PMC2639567          DOI: 10.1186/1757-1626-2-94

Source DB:  PubMed          Journal:  Cases J        ISSN: 1757-1626


  6 in total

1.  Oculopharyngeal muscular dystrophy. A familial disease of late life characterized by dysphagia and progressive ptosis of the evelids.

Authors:  M VICTOR; R HAYES; R D ADAMS
Journal:  N Engl J Med       Date:  1962-12-20       Impact factor: 91.245

Review 2.  Human genetics: lessons from Quebec populations.

Authors:  C R Scriver
Journal:  Annu Rev Genomics Hum Genet       Date:  2001       Impact factor: 8.929

3.  Clinical features of oculopharyngeal muscular dystrophy among Bukhara Jews.

Authors:  S C Blumen; P Nisipeanu; M Sadeh; A Asherov; F M Tomé; A D Korczyn
Journal:  Neuromuscul Disord       Date:  1993 Sep-Nov       Impact factor: 4.296

4.  Quality of life following surgical treatment of oculopharyngeal syndrome.

Authors:  Mireille Gervais; Dominique Dorion
Journal:  J Otolaryngol       Date:  2003-02

5.  Diagnosis and treatment of oculopharyngeal dystrophy: a report of three cases from the same family.

Authors:  V Munitiz; A Ortiz; L F Martinez de Haro; G Glover; B Ferri; M Montoya; P Parrilla
Journal:  Dis Esophagus       Date:  2003       Impact factor: 3.429

Review 6.  Oculopharyngeal muscular dystrophy: a late-onset polyalanine disease.

Authors:  B Brais
Journal:  Cytogenet Genome Res       Date:  2003       Impact factor: 1.636

  6 in total
  1 in total

1.  Oculopharyngeal muscular dystrophy as a rare cause of dysphagia.

Authors:  Sarah Werling; Bertold Schrank; Alexander J Eckardt; Anja Hauburger; Marcus Deschauer; Michaela Müller
Journal:  Ann Gastroenterol       Date:  2015 Apr-Jun
  1 in total

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