Quality of life following surgical treatment of oculopharyngeal syndrome.

Oculopharyngeal syndrome is a hereditary disease mostly affecting French Canadians. Cricopharyngeal myotomy and blepharoplasty are commonly performed on these patients. We reviewed the files of 20 patients who underwent these procedures between June 1986 and June 1999. The average perioperative stay was 4.7 days. The nine patients still alive were contacted and answered a telephone survey on their quality of life. None reported postoperative complications. Myotomy significantly improved the medical domain of their quality of life as confirmed by improvement in the dysphagia for solids, food incarceration, duration of meals, and choking during meals. The psychological domain also improved, namely, appetite and interest in food. The effects of blepharoplasty were also notable. Long-term satisfaction is reported by the majority of patients up to a maximum of 10 years postoperatively. In conclusion, simple procedures such as blepharoplasty and cricopharyngeal myotomy greatly improved the quality of life of these patients. We therefore recommend early interventions.