Literature DB >> 18513397

Single ventricle with persistent truncus arteriosus as two rare entities in an adult patient: a case report.

Inna Porter1, James Vacek.   

Abstract

INTRODUCTION: Single ventricle and truncus arteriosus are both rare congenital cardiac syndromes with limited survival. Their occurrence together is extremely uncommon and prolonged survival is exceptionally rare. We present the case of a patient who had both of these defects with survival to age 45. CASE
PRESENTATION: We describe the vase of a 45-year-old man with the unusual occurrence of two very rare congenital cardiac defects. He was found to have both truncus arteriosus and single ventricle with long survival. His history, clinical course, and anatomic findings are discussed along with the factors which may have contributed to his longevity, which is unique in the medical literature. His management reflected the state of medical knowledge at the time when he presented, and although alternate approaches may have been utilized if the patient presented today, this case does indicate the efficacy of the management options available at the time and place of the patient's contacts with the medical care system in Belarus. We discuss the findings, frequency, classification, and management of both of these congenital defects.
CONCLUSION: This case demonstrates that patients with very complex congenital cardiac disease may survive to adulthood, presenting challenges in both medical and surgical treatment. As the management of these patients is constantly evolving, and interventional techniques are improving, patients such as this with prolonged survival will be more common, with each case providing insights to future treatment. Challenges in management may include prior care provided in health care systems with limited resources.

Entities:  

Year:  2008        PMID: 18513397      PMCID: PMC2424060          DOI: 10.1186/1752-1947-2-184

Source DB:  PubMed          Journal:  J Med Case Rep        ISSN: 1752-1947


  17 in total

1.  Five- to fifteen-year follow-up after Fontan operation.

Authors:  D J Driscoll; K P Offord; R H Feldt; H V Schaff; F J Puga; G K Danielson
Journal:  Circulation       Date:  1992-02       Impact factor: 29.690

2.  COR TRILOCULARE BIAURICULARE: AN UNUSUAL ADULT HEART.

Authors:  J B Mehta; R F Hewlett
Journal:  Br Heart J       Date:  1945-01

3.  A case of congenital heart disease--truncus aorticus solitarius, single ventricle, and aberrant coronary drainage into the common ventricle.

Authors:  A J MILLER; O PREC; L AKMAN; L N KATZ; S GIBSON
Journal:  Am Heart J       Date:  1950-04       Impact factor: 4.749

4.  Successful diagnosis and surgical treatment of single ventricle, truncus arteriosus.

Authors:  R E Shaddy; E C McGough
Journal:  Ann Thorac Surg       Date:  1989-08       Impact factor: 4.330

5.  Single ventricle. Pathology, embryology, terminology and classification.

Authors:  R van Praagh; J A Plett; S van Praagh
Journal:  Herz       Date:  1979-04       Impact factor: 1.443

6.  Persistent truncus arteriosus. Report of survival to age of 52 years.

Authors:  J B Carter; L C Blieden; J E Edwards
Journal:  Minn Med       Date:  1973-04

7.  Influence of patient factors and ablative technologies on outcomes of radiofrequency ablation of intra-atrial re-entrant tachycardia in patients with congenital heart disease.

Authors:  John K Triedman; Mark E Alexander; Barry A Love; Kathryn K Collins; Charles I Berul; Laura M Bevilacqua; Edward P Walsh
Journal:  J Am Coll Cardiol       Date:  2002-06-05       Impact factor: 24.094

8.  Long-term follow-up in the unoperated univentricular heart.

Authors:  D S Moodie; D G Ritter; A J Tajik; W M O'Fallon
Journal:  Am J Cardiol       Date:  1984-04-01       Impact factor: 2.778

9.  Congenital heart disease among 815,569 children born between 1980 and 1990 and their 15-year survival: a prospective Bohemia survival study.

Authors:  M Samánek; M Vorísková
Journal:  Pediatr Cardiol       Date:  1999 Nov-Dec       Impact factor: 1.655

10.  Implications of implantable cardioverter defibrillator therapy in congenital heart disease and pediatrics.

Authors:  Mark E Alexander; Frank Cecchin; Edward P Walsh; John K Triedman; Laura M Bevilacqua; Charles I Berul
Journal:  J Cardiovasc Electrophysiol       Date:  2004-01
View more
  1 in total

1.  An infant with truncus arteriosus with situs inversus with single atrium: A case report.

Authors:  Parveen Kumar; A Devi; Gopal Ghosh
Journal:  J Cardiol Cases       Date:  2016-12-06
  1 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.