Literature DB >> 18157541

Deformity correction for vitamin D-resistant hypophosphatemic rickets of adults.

Hidenori Matsubara1, Hiroyuki Tsuchiya, Tamon Kabata, Keisuke Sakurakichi, Koji Watanabe, Katsuro Tomita.   

Abstract

We performed correction for bowing deformity of the lower extremities due to vitamin D-resistant hypophosphatemic rickets of three adults, six segments. The operative method was gradual correction and lengthening using distraction osteogenesis by Ilizarov external fixator or Heidelberg external fixator. The orders of the corrections were simultaneous correction of the bilateral femur for one patient, simultaneous correction of the ipsilateral leg for one patient, and diagonal correction of the bilateral leg for one patient. The mean correction angle was 30.5 degrees. The mean external fixation period was 146 days. Each orders of the corrections had its merits and demerits. All patients obtained a physiological alignment and good bone formation by taking Vitamin D and oral phosphate supplements even an adult patient. All the patients had articular pain, such as hip, knee, and ankle, however, these pains healed up. All the patients were satisfied with the outcomes at the time of the final follow-up interview in terms of their cosmetic improvement. Distraction osteogenesis for bowing deformity of the lower extremities due to vitamin D-resistant hypophosphatemic rickets was very effective method and could be applied to adult patients. However, the order of the corrections should be considered carefully depending on each patient.

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Year:  2007        PMID: 18157541     DOI: 10.1007/s00402-007-0548-8

Source DB:  PubMed          Journal:  Arch Orthop Trauma Surg        ISSN: 0936-8051            Impact factor:   3.067


  3 in total

1.  Results of deformity correction in children with X-linked hereditary hypophosphatemic rickets by external fixation or combined technique.

Authors:  Arnold Popkov; Anna Aranovich; Dmitry Popkov
Journal:  Int Orthop       Date:  2015-07-07       Impact factor: 3.075

2.  The significance of serum phosphate level on healing index and its relative effects in skeletally immature and mature patients with hypophosphatemic rickets.

Authors:  Sang-Heon Song; Hanna Lee; Ji-Min Jeong; Woo-In Cho; Sung Eun Kim; Hae-Ryong Song
Journal:  Biomed Res Int       Date:  2014-04-24       Impact factor: 3.411

3.  Identification of a Novel Missense Mutation of the PHEX Gene in a Large Chinese Family with X-Linked Hypophosphataemia.

Authors:  Yanting Yang; Yuanda Wang; Ying Shen; Mohan Liu; Siyu Dai; Xiaodong Wang; Hongqian Liu
Journal:  Front Genet       Date:  2022-02-17       Impact factor: 4.599

  3 in total

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