Literature DB >> 1770774

Arginine remains an essential amino acid after liver transplantation in urea cycle enzyme deficiencies.

D Rabier1, C Narcy, J Bardet, P Parvy, J M Saudubray, P Kamoun.   

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Year:  1991        PMID: 1770774     DOI: 10.1007/bf01811681

Source DB:  PubMed          Journal:  J Inherit Metab Dis        ISSN: 0141-8955            Impact factor:   4.982


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  4 in total

1.  Persistent acitrullinemia after liver transplantation for carbamylphosphate synthetase deficiency.

Authors:  M Tuchman
Journal:  N Engl J Med       Date:  1989-06-01       Impact factor: 91.245

2.  Liver transplantation for ornithine transcarbamylase deficiency in a girl.

Authors:  C Largillière; D Houssin; F Gottrand; C Mathey; A Checoury; D Alagille; J P Farriaux
Journal:  J Pediatr       Date:  1989-09       Impact factor: 4.406

3.  Liver disorders in children: the indications for liver replacement in parenchymal and metabolic diseases.

Authors:  A P Mowat
Journal:  Transplant Proc       Date:  1987-08       Impact factor: 1.066

4.  Source and fate of circulating citrulline.

Authors:  H G Windmueller; A E Spaeth
Journal:  Am J Physiol       Date:  1981-12
  4 in total
  8 in total

1.  Orthotopic liver transplantation in liver-based metabolic disorders.

Authors:  A P Mowat
Journal:  Eur J Pediatr       Date:  1992       Impact factor: 3.183

2.  Metabolism of citrulline in man.

Authors:  D Rabier; P Kamoun
Journal:  Amino Acids       Date:  1995-12       Impact factor: 3.520

3.  Liver transplantation for citrullinaemia improves intellectual function.

Authors:  J M Fletcher; R Couper; D Moore; R Coxon; S Dorney
Journal:  J Inherit Metab Dis       Date:  1999-06       Impact factor: 4.982

4.  Hepatocyte gene therapy in a large animal: a neonatal bovine model of citrullinemia.

Authors:  B Lee; J A Dennis; P J Healy; B Mull; L Pastore; H Yu; E Aguilar-Cordova; W O'Brien; P Reeds; A L Beaudet
Journal:  Proc Natl Acad Sci U S A       Date:  1999-03-30       Impact factor: 11.205

5.  Liver transplantation for the treatment of urea cycle disorders.

Authors:  P F Whitington; E M Alonso; J T Boyle; J P Molleston; P Rosenthal; J C Emond; J M Millis
Journal:  J Inherit Metab Dis       Date:  1998       Impact factor: 4.982

Review 6.  Arginine metabolism: nitric oxide and beyond.

Authors:  G Wu; S M Morris
Journal:  Biochem J       Date:  1998-11-15       Impact factor: 3.857

Review 7.  Response to treatment in hereditary metabolic disease: 1993 survey and 10-year comparison.

Authors:  E Treacy; B Childs; C R Scriver
Journal:  Am J Hum Genet       Date:  1995-02       Impact factor: 11.025

8.  Liver-directed adeno-associated virus serotype 8 gene transfer rescues a lethal murine model of citrullinemia type 1.

Authors:  R J Chandler; T N Tarasenko; K Cusmano-Ozog; Q Sun; V R Sutton; C P Venditti; P J McGuire
Journal:  Gene Ther       Date:  2013-10-17       Impact factor: 5.250

  8 in total

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